Steatocystoma multiplex. Report of a florid case and a review

Egbert, Barbara M.

doi:10.1001/archderm.115.3.334

Cited by 19 publications

(3 citation statements)

References 9 publications

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“…COMMENT Steatocystoma multiplex is a nevoid tumor composed of sebaceous duct and gland.13 Treatment is difficult for florid cases. 4 Although plastic surgery provides good results in some cases,56 fairly large incisional scars can result.7 In this florid case of steatocystoma multiplex, we present a simple, time-saving treatment: aspiration of the oily material in the cyst by means of a syringe connected to an 18-gauge needle and the subsequent scraping of the cyst wall with the tip of the needle.…”

Section: Therapeutic Solutionmentioning

confidence: 98%

Aspiration Therapy in Steatocystoma Multiplex

Satô

Shibuya²,

Taguchi³

et al. 1993

Arch Dermatol

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In October 1982, a 41-year-old man was seen because of multiple soft tumors on the upper half of his body. These tumors were up to 3 cm in diameter. His parents were not consanguineous. His family, including his 18-and 19-year-old children, had no history of similar lesions. At 16 years of age, our patient first noticed subcutaneous nodules on his neck. Since then, the number and size of the nodules increased.When he was 20 years of age, there were many nodules on his head, neck, trunk, and upper extremities. The nodules continually discharged oily material and became inflamed and tender. Following a diagnosis of steatocystoma multiplex, 25 cysts on his head were surgically excised with 750 mL ofblood loss. The oily material was sterile. About 75 smaller cysts on the trunk were excised and drained, and the walls of cyst were treated with 60% trichloroacetic acid. Findings from his physical examination showed mild liver dysfunction, mild hyperlipidemia, and a duodenal ulcer, but other clinical and laboratory data showed normal results.In 1991, he requested removal of the remaining cysts ( Fig 1). About 10 cysts (diameter, 1 to 3 cm) were excised from the arm, neck, and forehead during the next 2 months. However, we realized that the procedure was very time consuming and stressful and that total surgical removal of all of the cysts in such a florid case of steatocystoma multiplex was not feasi¬ ble. We then attempted aspiration. From June through Sep¬ tember 1991, cysts larger than 1 cm in diameter were aspi¬ rated and scraped with a syringe connected to an 18-gauge needle (caliber, 1.20 mm; bevel, 18 degrees; Terum, Tokyo, Japan) (Fig 2). The result was satisfactory, and the patient's psychological condition showed much improvement. In January 1992, the smaller remaining cysts were incised and drained. By March 1992, the larger cysts that were as¬ pirated and scraped 10 months before did not enlarge (Fig 3), but the smaller ones that were incised and drained had already started to enlarge (Fig 3). Biopsy specimens were obtained from cysts that were aspirated and scraped and those that were incised and drained. THERAPEUTIC CHALLENGEAlthough the observation period of 10 months is short and small cysts cannot be treated well with only aspiration, our method for the treatment of larger cysts of steatocystoma multiplex could improve the cosmetic appearance of the pa¬ tient's facial lesions with little scarring. THERAPEUTIC SOLUTIONWhen the cysts were aspirated, the tip of an 18-gauge nee¬ dle was inserted into the cyst. During aspiration, the tip was moved and rotated to scrape off the sebaceous glands in the cyst wall. In order to minimize inflammatory responses due to the leak of oily material and injury to blood vessels, we avoided multiple punctures of the cyst walls and tried to scrape them gently, which we could feel. The aspirated yel¬ low oily material contained many clusters of vellus hairs and keratin. One mature hair about 5 cm long was aspirated from a cyst. It was difficult to aspirate oily material with...

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Section: Therapeutic Solutionmentioning

confidence: 98%

Aspiration Therapy in Steatocystoma Multiplex

Satô

Shibuya²,

Taguchi³

et al. 1993

Arch Dermatol

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“…11 Egebert reported a severe case with extensive cysts in which hospitalization, oral antibiotics, incision and drainage, and electrocautery under general anesthesia. 12 According to the literature, this is the first report that directly compares the outcomes of three different treatments performed for a patient with SM. In our case, cyst removal by simple incision and drainage (A) and incision and drainage followed by electrodessication (B) both yielded the best cosmetic outcomes at two-week follow up (Figure 3).…”

Section: Case Reportmentioning

confidence: 99%

Steatocystoma Multiplex: Case Report and Review of Treatment

Amin

Hashim²

2018

J of Skin

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Steatocystoma multiplex, an uncommon autosomal dominant disorder, is characterized by numerous asymptomatic skin-colored cystic nodules. The leading hypothesis regarding the pathophysiology of this disease involves a defect at the pilosebaceous duct junction, which leads to cyst formation. Herein, we describe a case of a male patient that presented with steatocystoma multiplex. We examine the cosmetic outcomes of different techniques used in his treatment as well as review the varied therapeutic options available to such patients, including surgical removal, needle aspiration, cryotherapy, isotretinoin, and CO2 laser treatment.

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“…Clinical conditions that have been associated with steatocystoma multiplex included acrokeratosis verruciformis of Hopf, koilonychia, pachyonchia congenita, hypothyroidism, hidradenitis suppurativa, hypohidrosis, hypotrichosis, ichthyosis, lichen planus, Gardners syndrome, and natal teeth 8–10 …”

Section: Resolutionmentioning

confidence: 99%