Status Epilepticus Amauroticus Revisited

Abstract

To describe the clinical, electrographic, and radiographic features of status epilepticus amauroticus, or homonymous hemianopsia associated with partial status epilepticus, in 3 patients with subsequent resolution of radiographic abnormalities and visual deficits.

Mitochondrial Myopathy, Encephalopathy, Lactic acidosis and Stroke-Like Episodes Syndrome Presenting With Anton-Babinski Syndrome and Concurrent Occipital Lobe Seizures

“…Neuroimaging in our patient revealed hyperintensity on DWI as well as FLAIR and T2 signal along the right occipital cortex, but the corresponding occipital region had iso-density in ADC values, which rules out restricted water diffusion as in an ischemic stroke. This temporal ADC evolution in status epilepticus contrasts with the pattern seen in ischemic stroke, where ADC value is significantly reduced in the acute phase, followed by a gradual increase in the following days [16]. The local cellular disturbance initiated by a seizure may lead to fluctuations and shift of intra-and extra-cellular water, possibly resulting in cell swelling.…”

“…DWI abnormalities in seizures result from a combination of impaired energy metabolism and hemodynamic changes rather than hypoxia/anoxia present in acute ischemic stroke. Therefore, the DWI in seizures frequently shows reversibility [16].…”

Mitochondrial Myopathy, Encephalopathy, Lactic acidosis and Stroke-Like Episodes Syndrome Presenting With Anton-Babinski Syndrome and Concurrent Occipital Lobe Seizures

“…Neuroimaging in our patient revealed hyperintensity on DWI as well as FLAIR and T2 signal along the right occipital cortex, but the corresponding occipital region had iso-density in ADC values, which rules out restricted water diffusion as in an ischemic stroke. This temporal ADC evolution in status epilepticus contrasts with the pattern seen in ischemic stroke, where ADC value is significantly reduced in the acute phase, followed by a gradual increase in the following days [16]. The local cellular disturbance initiated by a seizure may lead to fluctuations and shift of intra-and extra-cellular water, possibly resulting in cell swelling.…”

“…DWI abnormalities in seizures result from a combination of impaired energy metabolism and hemodynamic changes rather than hypoxia/anoxia present in acute ischemic stroke. Therefore, the DWI in seizures frequently shows reversibility [16].…”

Transient Homonymous Superior Quadrantanopsia in Nonketotic Hyperglycemia: A Case Report and Systematic Review

“… 14 However, EEG rarely produces discernible findings in patients with focal epilepsy presenting with visual field defects. 15 Furthermore, although not attributed to seizures, diabetes can by itself result in neuronal dysfunction secondary to metabolic derangement. 16 Indeed, our systematic review found that only half of the patients showed epileptic discharges.…”

Mitochondrial Myopathy, Encephalopathy, Lactic acidosis and Stroke-Like Episodes Syndrome Presenting With Anton-Babinski Syndrome and Concurrent Occipital Lobe Seizures

“…Neuroimaging in our patient revealed hyperintensity on DWI as well as FLAIR and T2 signal along the right occipital cortex, but the corresponding occipital region had iso-density in ADC values, which rules out restricted water diffusion as in an ischemic stroke. This temporal ADC evolution in status epilepticus contrasts with the pattern seen in ischemic stroke, where ADC value is significantly reduced in the acute phase, followed by a gradual increase in the following days [16]. The local cellular disturbance initiated by a seizure may lead to fluctuations and shift of intra-and extra-cellular water, possibly resulting in cell swelling.…”

“…DWI abnormalities in seizures result from a combination of impaired energy metabolism and hemodynamic changes rather than hypoxia/anoxia present in acute ischemic stroke. Therefore, the DWI in seizures frequently shows reversibility [16].…”

Transient Homonymous Superior Quadrantanopsia in Nonketotic Hyperglycemia: A Case Report and Systematic Review

“… 14 However, EEG rarely produces discernible findings in patients with focal epilepsy presenting with visual field defects. 15 Furthermore, although not attributed to seizures, diabetes can by itself result in neuronal dysfunction secondary to metabolic derangement. 16 Indeed, our systematic review found that only half of the patients showed epileptic discharges.…”

Mitochondrial Myopathy, Encephalopathy, Lactic acidosis and Stroke-Like Episodes Syndrome Presenting With Anton-Babinski Syndrome and Concurrent Occipital Lobe Seizures

“…Neuroimaging in our patient revealed hyperintensity on DWI as well as FLAIR and T2 signal along the right occipital cortex, but the corresponding occipital region had iso-density in ADC values, which rules out restricted water diffusion as in an ischemic stroke. This temporal ADC evolution in status epilepticus contrasts with the pattern seen in ischemic stroke, where ADC value is significantly reduced in the acute phase, followed by a gradual increase in the following days [16]. The local cellular disturbance initiated by a seizure may lead to fluctuations and shift of intra-and extra-cellular water, possibly resulting in cell swelling.…”

“…DWI abnormalities in seizures result from a combination of impaired energy metabolism and hemodynamic changes rather than hypoxia/anoxia present in acute ischemic stroke. Therefore, the DWI in seizures frequently shows reversibility [16].…”

Transient Homonymous Superior Quadrantanopsia in Nonketotic Hyperglycemia: A Case Report and Systematic Review

“… 14 However, EEG rarely produces discernible findings in patients with focal epilepsy presenting with visual field defects. 15 Furthermore, although not attributed to seizures, diabetes can by itself result in neuronal dysfunction secondary to metabolic derangement. 16 Indeed, our systematic review found that only half of the patients showed epileptic discharges.…”