Síndrome de obstrucción intestinal distal en pacientes adultos con fibrosis quística: Casos clínicos

Abstract

Distal intestinal obstruction syndrome. Report of two cases with cystic fibrosis Distal Intestinal Obstruction Syndrome (DIOS) has a 16% incidence among patients with Cystic Fibrosis (CF). It is characterized by an intestinal obstruction secondary to fecal impaction in distal ileum or cecum. We report two adult patients with DIOS. A female with CF and subjected to a lung transplantation at the age of 13 years. Five years later, she consulted for an intestinal obstruction. She was treated conservatively with a good clinical evolution. She had a new episode of DIOS eight months later, that was also treated conservatively. A 31 year-old male, subjected to bilateral lung transplantation nine years before, that was admitted to the hospital for a bronchiolitis. Three days after admission he started with a intestinal obstruction, that was diagnosed as a DIOS. He was managed conservatively with a good clinical response.

Impacto de la afectación hepatobiliopancreática y el estatus nutricional en la sobrevida de adultos con fibrosis quística

“…6 La FQ presenta grandes variaciones fenotípicas, siendo sus manifestaciones más prevalentes la enfermedad pulmonar y la insuficiencia pancreática exócrina. Entre las manifestaciones gastrointestinales, se destacan las del tubo digestivo (íleo meconial, obstrucción intestinal), 7,8 vías biliares e hígado (colelitiasis, cirrosis biliar) 9, 11 y páncreas (pancreatitis aguda, insuficiencia pancreática exocrina y endócrina). 11,14 La enfermedad hepática asociada a la fibrosis quística (EHAFQ) constituye la causa de muerte no pulmonar más importante, representando entre 2,5 a 3,3% de la mortalidad.…”