“…In most cases, such as in ours, cholesteatoma is the first suspect. e differential diagnoses of a neuroendocrine adenoma include jugulotympanic paraganglioma, vascular malformations, acoustic neurinoma, meningioma, endolymphatic sac papillary tumor, rhabdomyosarcoma, teratoid tumor, and adenocarcinoma [8][9][10]. However, histologic, imaging, and immunohistochemical investigations allow for an accurate diagnosis [2].…”