s Hepatovenocaval Syndrome a Different Entity from Budd-Chiari Syndrome in Children?

Abstract

Hepatovenocaval syndrome (HVCS) mostly affected younger children, especially girls. BCS usually affected older age groups with pro-coagulant disorders who responded to anticoagulation and diuretic. Further studies are needed to compare both conditions.

Budd-Chiari Syndrome during Long-term Follow-up after Allogeneic Umbilical Cord Blood Transplantation

“…Other possible causes of Budd-Chiari syndrome in this case were suspected to be calcifications after liver abscesses ( 8 ) and liver deformation. These causes often lead to the development of secondary Budd-Chiari syndrome due to compression of the IVC by large structures exhibiting calcification or liver deformation (especially enlargement of the caudate lobe) ( 9 - 13 ), and they were ruled out in this case because the calcifications were small and there was no clear compression of the IVC due to liver deformation. As the patient had a history of multiple liver abscesses, the possibility of hepatic vena cava syndrome (HVCS) was also considered, although this is rare outside developing countries.…”

“…As the patient had a history of multiple liver abscesses, the possibility of hepatic vena cava syndrome (HVCS) was also considered, although this is rare outside developing countries. HVCS is a disease in which the main lesion arises from stenosis and occlusion after healing of focal thrombophlebitis at the confluence of the hepatic vein and the IVC due to bacteremia associated with poor hygiene ( 9 , 14 - 16 ).…”