Retinal vasculitis in Susac syndrome: case report

Susac syndrome: diverse clinical findings and treatment

“…Susac syndrome has an unknown etiology and is associated with varying outcomes (2,4,6) . If not suspected of having the syndrome, the diagnosis may be delayed.…”

“…When arteriolar abnormalities are observed close to the central vision, symptoms of visual loss are more evident and the diagnosis may be faster. However, most cases have peripheral arteriolar micro-occlusive events, resulting in late ophthalmologic evaluation (4) . Multifocal arteriolar wall hyperfluorescence and peripheral branch artery occlusion can occur in normal-appearing fundus.…”

“…The natural history and outcomes of SS are not fully understood. The disease may be active for several months and the time to remission can be long (4) . After remission it results in various cognitive and functional damages.…”

Síndrome de Susac en un paciente con colitis ulcerosa

“…Sin embargo, la etiología de la enfermedad todavía no está clara 3 . Se caracteriza por una microangiopatía en las arteriolas con oclusión recurrente de la arteria retiniana, y afecta principalmente a las mujeres y personas sanas de mediana edad 4 . Aunque la comprensión de la inmunopatogenia es incompleta, la evidencia preliminar sugiere que los anticuerpos contra células endoteliales pueden desempeñar un papel muy importante en el desarrollo de esta patología, ya que refleja el daño que se produce sobre las células endoteliales 5,6 .…”

Susac's syndrome: A case of simultaneous development of all three components of the triad

“…It is characterized by microangiopathy involving the arterioles of the brain, retina and cochlea [3]. The syndrome can be observed as recurrent multiple retinal artery occlusion, hearing loss and encephalopathy without systemic manifestation in healthy people of middle age, predominantly women [4].…”