Retinal Detachments in Incontinentia Pigmenti

Incontinentia Pigmenti: A Comprehensive Review and Update

“…An avascular peripheral retina is a significant feature of IP and is often considered the classic retinal finding (Figure 2). 4,31,34 Large areas of the peripheral retina may become avascular, similar to the findings in retinopathy of prematurity. As with most ischemic retinal processes, neovascularization can often be found at the edges of the avascular retina and can lead to the blinding complications of IP such as hemorrhages and retinal detachment.…”

Incontinentia Pigmenti: A Comprehensive Review and Update

“…An avascular peripheral retina is a significant feature of IP and is often considered the classic retinal finding (Figure 2). 4,31,34 Large areas of the peripheral retina may become avascular, similar to the findings in retinopathy of prematurity. As with most ischemic retinal processes, neovascularization can often be found at the edges of the avascular retina and can lead to the blinding complications of IP such as hemorrhages and retinal detachment.…”

Ophthalmic evaluation, treatment, and follow-up of two cases of incontinentia pigmenti

“…Cataracts are also a common feature of the disease and, in many cases, are the ocular symptoms that bring the child to the ophthalmologist. When the cataract is combined with retinal detachment, surgical results can be very poor (8) , as observed in Case 1. Ischemia of the peripheral retina with new vessel proliferation, as observed in Case 2, is one of the most common features of IP and, if not treated, is probably responsible for retinal detachment.…”

Combined rhegmatogenous and tractional retinal detachment in a child with incontinentia pigmenti managed by scleral imbrication with scleral buckle

“…A wide array of ophthalmic manifestations associated with IP have been reported and this includes nystagmus, strabismus, microphthalmos, cataract, glaucoma, optic atrophy, foveal hypoplasia, retinal avascularity, retinal neovascularisation, vitreous haemorrhage and tractional retinal detachment 8–10. Ophthalmic manifestations of IP in infants are vision threatening and their clinical presentation can at times mimic retinopathy of prematurity (ROP), familial exudative vitreoretinopathy (FEVR) and Norrie’s disease 11.…”

Incontinentia Pigmenti: A Comprehensive Review and Update

“…An avascular peripheral retina is a significant feature of IP and is often considered the classic retinal finding (Figure 2). 4,31,34 Large areas of the peripheral retina may become avascular, similar to the findings in retinopathy of prematurity. As with most ischemic retinal processes, neovascularization can often be found at the edges of the avascular retina and can lead to the blinding complications of IP such as hemorrhages and retinal detachment.…”

Ophthalmic evaluation, treatment, and follow-up of two cases of incontinentia pigmenti

“…Cataracts are also a common feature of the disease and, in many cases, are the ocular symptoms that bring the child to the ophthalmologist. When the cataract is combined with retinal detachment, surgical results can be very poor (8) , as observed in Case 1. Ischemia of the peripheral retina with new vessel proliferation, as observed in Case 2, is one of the most common features of IP and, if not treated, is probably responsible for retinal detachment.…”

Combined rhegmatogenous and tractional retinal detachment in a child with incontinentia pigmenti managed by scleral imbrication with scleral buckle

“…A wide array of ophthalmic manifestations associated with IP have been reported and this includes nystagmus, strabismus, microphthalmos, cataract, glaucoma, optic atrophy, foveal hypoplasia, retinal avascularity, retinal neovascularisation, vitreous haemorrhage and tractional retinal detachment 8–10. Ophthalmic manifestations of IP in infants are vision threatening and their clinical presentation can at times mimic retinopathy of prematurity (ROP), familial exudative vitreoretinopathy (FEVR) and Norrie’s disease 11.…”

Incontinentia Pigmenti: A Comprehensive Review and Update

“…An avascular peripheral retina is a significant feature of IP and is often considered the classic retinal finding (Figure 2). 4,31,34 Large areas of the peripheral retina may become avascular, similar to the findings in retinopathy of prematurity. As with most ischemic retinal processes, neovascularization can often be found at the edges of the avascular retina and can lead to the blinding complications of IP such as hemorrhages and retinal detachment.…”

Ophthalmic evaluation, treatment, and follow-up of two cases of incontinentia pigmenti

“…Cataracts are also a common feature of the disease and, in many cases, are the ocular symptoms that bring the child to the ophthalmologist. When the cataract is combined with retinal detachment, surgical results can be very poor (8) , as observed in Case 1. Ischemia of the peripheral retina with new vessel proliferation, as observed in Case 2, is one of the most common features of IP and, if not treated, is probably responsible for retinal detachment.…”

Combined rhegmatogenous and tractional retinal detachment in a child with incontinentia pigmenti managed by scleral imbrication with scleral buckle

“…A wide array of ophthalmic manifestations associated with IP have been reported and this includes nystagmus, strabismus, microphthalmos, cataract, glaucoma, optic atrophy, foveal hypoplasia, retinal avascularity, retinal neovascularisation, vitreous haemorrhage and tractional retinal detachment 8–10. Ophthalmic manifestations of IP in infants are vision threatening and their clinical presentation can at times mimic retinopathy of prematurity (ROP), familial exudative vitreoretinopathy (FEVR) and Norrie’s disease 11.…”