Recurrent lower respiratory tract infections in a 14‐year‐old boy with tracheobronchomegaly (Mounier‐Kuhn syndrome)

Abstract

Summary. Tracheobronchomegaly (Mounier-Kuhn syndrome) is characterized by dilatation of the central airways, tracheobronchial outpouchings, and chronic tracheobronchitis. Most cases are diagnosed in adulthood. We report the clinical, radiographic, and bronchoscopic findings in a 14-year-old boy with tracheobronchomegaly, ptosis of the right eyelid, and redundant skin and mucosa of the upper lip, who presented with a 2-year history of recurrent lower respiratory tract infections. Pediatricians should be aware of the possibility that tracheobronchomegaly may cause clinical symptoms in childhood and adolescence. Pediatr Pulmonol. 2000; 29: 476-479.

Coincidence of Tracheobronchomegaly (Mounier-Kuhn Syndrome) and Juvenile Idiopathic Arthritis

“…muscle tissue of the trachea and main bronchi. Although there is a known association with Ehlers-Danlos in adults and some cases in children related to different connective tissue diseases, the majority of patients do not have either of these diseases suggesting a further, as yet unknown, factor in the aetiology [1,4,7]. We report a case of a 4-year-old adopted Indian girl who was studied because of shortness of breath, recurrent respiratory tract infections with morning cough and joint pain.…”

Tracheobronchomegaly (Mounier-Kuhn Syndrome) in a 43-Year-Old Male: A Case Report

“……”

Development of Tracheobronchomegaly during Mechanical Ventilation: An Unusual Case Report / Mekanik Ventilasyon Sırasında Gelişen Trakeobronkomegali: Ender Bir Olgu Sunumu

“…The clinical features were described by Mounier-Kuhn. Destruction or atrophy of the elastic tissue and smooth muscle of the trachea is a dominant pathological finding (2), with an incidence of about 1/500 (3).The disease predominantly occurs in men in their third and fourth decades of life (4).…”