“…However a higher tumor risk is seen in a minority of individuals who do demonstrate abnormalities in this region [Hoyme et al, ; Shuman et al, ]. A review of the available literature identified only seven previous case reports of pheochromocytoma occurring up to the age of 20 years in any of BWS (n = 2, both bilateral) [Bemurat et al, ; Baldisserotto et al, ], IH (n = 4) [Schnakenburg et al, ; van den Akker et al, ; Kalish et al, ; Pikilidou et al, ], and MGWpatUPD (n = 1, bilateral) [Wilson et al, ] which are summarized in Table . The relative risk of pheochromocytoma in MGWpatUPD versus isolated 11p15 patUPD syndromes is not clear from the knowledge base to date.…”