Pulmonary arterial hypertension: diagnosis and treatment

Abstract

Pulmonary arterial hypertension is one of the clinical groups of arterial hypertension. It is a rare, chronic disease with a very poor prognosis. Diagnostic procedures ruling out different causes of present symptoms and other forms of pulmonary hypertension are difficult and specific. Current European guidelines recommend combined treatment with endothelin receptor antagonist, prostanoids, and phosphodiesterase type 5 inhibitors.

Idiopathic pulmonary fibrosis with complication of severe respiratory failure, right heart failure, and steroid induced diabetes – qualification for lung transplantation as a matter of urgency

“…The echocardiogram showed marginally thicker muscle of the left ventricle, widening of the right ventricle, mildly increased right atrial cavity, mild tricuspid regurgitation, and features of pulmonary arterial hypertension (RSVP estimated 103 mm Hg, shortened AcT 54 ms). Features of overload of the right ventricle were not present in the previous study carried out three months earlier (AcT 135 ms, VCI 1.4/0.8 cm) [6,7].…”

“…A doctor of the Clinical Department of Silesian Medical University was contacted, and the deadline, on 16.07.2014, for the patient hospitalisation was re-established. In accordance with the recommendations sildenafil was included in the treatment at a dose of 2 × 25 mg [7,8] and methylprednisolone was discontinued. It was agreed that the patient would visit the Clinic for oxygen therapy in order to qualify for home oxygen therapy and to secure the patient's travel from Warsaw to Zabrze.…”