Pseudoainhum associated with linear scleroderma

Pseudoainhum numa doente com Doença Mista do Tecido Conjuntivo: uma associação incomum Pseudoainhum in a patient with Mixed Connective Tissue Disease: an uncommon association

“…It is conceivable that vascular anomalies observed in RP and SSc, drive the acrosclerotic changes in the same way that they eventually cause pseudoainhum, in some patients, as previously noted. 8 The same is inferable in our case, as sclerosis was significantly worse in the 2 afflicted fingers compared to the others.…”

Unna Thost syndrome: a case report

“…Worsening of the clinical condition or increasing relapses occurs during the cold periods of the year. 17 The histopathologic alterations in Unna-Thost PPK are non-specific. They typically lack epidermolysis, which is an important factor of differentiation from Vorner's epidermolytic palmoplantar keratoderma.…”

Pseudoainhum in a patient with tuberous sclerosis complex: a case report and review of the literature

“…2,29,42 This report describes a case of pseudoainhum presenting with properties characteristic of TSC. This association, which has not been previously Disorders of abnormal keratinization Psoriasis [15][16][17] Pityriasis rubra pilaris 18 Porokeratosis of Mibelli 19 Congenital linear porokeratosis 20 Focal acral hyperkeratosis and angiodysplasia 21 Lamellar ichthyosis [22][23][24] Keratosis palmoplantaris with polydactyly and eosinophilia 25 Keratoma hereditarium dissipatum palmare et plantare (Buschke-Fischer-Brauer) 26 Keratoderma hereditarium mutilans (Vohwinkel) [27][28][29][30][31][32] Progressive symmetric erythrokeratoderma (PSEK) 4 Keratosis linearis with ichthyosis congenita and sclerosing keratoderma (KLICK) 5 Keratosis palmoplantaris transgradiens of Siemens (mal de Meleda) 6,33 Clouston's syndrome 34 Ectodermal dysplasia syndrome (with cataracts, alopecia, sclerodactyly) 35 Papillon-Lefevre syndrome 36 Loricrin keratoderma 32 Metabolic and neurologic diseases Isolated polyneuropathy 37 Gout disease 38 Alcohol-toxic polyneuropathy 9 Erythropoietic protoporphyria 11 Plica neuropathica, hair matting, schizophrenia 10 Reynolds syndrome and breast cancer 14 Connective tissue diseases Rheumatoid arthritis 39 Discoid lupus erythematosus 40 Localized scleroderma 41,42 Bullous disease Hereditary bullous acrokeratotic poikiloderma of Wea...…”