Primary Orbital Hemangiopericytoma

Primary Orbital Hemangiopericytoma: An Unusual Cause of Unilateral Proptosis

“…The chief complaint in our patient was perception of a rapid expanding intra-orbital mass resulting in painless proptosis of the left eye. Many previous reports described tumour growth as causing relatively little disturbance of visual function, which was not the case in our patient who lost vision in his affected eye 4,[6][7][8] . The tumour tends to be non-tender and non-pulsatile as it was the case in our patient.…”

Primary Orbital Hemangiopericytoma: An Unusual Cause of Unilateral Proptosis

“…The chief complaint in our patient was perception of a rapid expanding intra-orbital mass resulting in painless proptosis of the left eye. Many previous reports described tumour growth as causing relatively little disturbance of visual function, which was not the case in our patient who lost vision in his affected eye 4,[6][7][8] . The tumour tends to be non-tender and non-pulsatile as it was the case in our patient.…”

Intraocular Hemangiopericytoma

“…In the present case, no distinct mitotic figures were seen, suggesting little activity of the tumor, which was contrary to the clinical findings of malignancy including invasion into the iris of this neoplasm. Even so, a case histologically diagnosed as a benign hemangiopericytoma resulted in death due to metastatic spread [15]. …”

Unusual occurrence of orbital hemangiopericytoma in the zygomatic bone of an adolescent: a case report

“…HPC is a rare vascular soft-tissue tumor that can develop anywhere in the body that has blood vessels, most notably in lower extremities, pelvic fossa, retroperitoneum and nasopharynx [ 5 ]. HPC rarely involves the orbit [ 6 ] and constitutes only 1.57% of orbital tumors [ 7 ]. Likewise, bones are uncommonly involved in HPC, which accounts for 4.7% of bone tumors [ 2 , 3 ].…”

“…The treatment of choice for HPC is complete en-bloc surgical excision whenever possible, because these tumors are most often circumscribed or enclosed by a pseudocapsule [ 7 , 11 ]. Completeness of surgical resection positively affects survival, while incomplete excision (piece-meal resection) or incisional biopsy are associated with local spread, recurrence and metastasis [ 7 , 11 ]. However, as in our case, complete tumor resection can occasionally be challenging due to its friable and highly-vascular nature [ 21 ].…”

Primary Orbital Hemangiopericytoma: An Unusual Cause of Unilateral Proptosis

“…The chief complaint in our patient was perception of a rapid expanding intra-orbital mass resulting in painless proptosis of the left eye. Many previous reports described tumour growth as causing relatively little disturbance of visual function, which was not the case in our patient who lost vision in his affected eye 4,[6][7][8] . The tumour tends to be non-tender and non-pulsatile as it was the case in our patient.…”

Intraocular Hemangiopericytoma

“…In the present case, no distinct mitotic figures were seen, suggesting little activity of the tumor, which was contrary to the clinical findings of malignancy including invasion into the iris of this neoplasm. Even so, a case histologically diagnosed as a benign hemangiopericytoma resulted in death due to metastatic spread [15]. …”

Unusual occurrence of orbital hemangiopericytoma in the zygomatic bone of an adolescent: a case report

“…HPC is a rare vascular soft-tissue tumor that can develop anywhere in the body that has blood vessels, most notably in lower extremities, pelvic fossa, retroperitoneum and nasopharynx [ 5 ]. HPC rarely involves the orbit [ 6 ] and constitutes only 1.57% of orbital tumors [ 7 ]. Likewise, bones are uncommonly involved in HPC, which accounts for 4.7% of bone tumors [ 2 , 3 ].…”

“…The treatment of choice for HPC is complete en-bloc surgical excision whenever possible, because these tumors are most often circumscribed or enclosed by a pseudocapsule [ 7 , 11 ]. Completeness of surgical resection positively affects survival, while incomplete excision (piece-meal resection) or incisional biopsy are associated with local spread, recurrence and metastasis [ 7 , 11 ]. However, as in our case, complete tumor resection can occasionally be challenging due to its friable and highly-vascular nature [ 21 ].…”

Primary Orbital Hemangiopericytoma: An Unusual Cause of Unilateral Proptosis

“…The chief complaint in our patient was perception of a rapid expanding intra-orbital mass resulting in painless proptosis of the left eye. Many previous reports described tumour growth as causing relatively little disturbance of visual function, which was not the case in our patient who lost vision in his affected eye 4,[6][7][8] . The tumour tends to be non-tender and non-pulsatile as it was the case in our patient.…”

Intraocular Hemangiopericytoma

“…In the present case, no distinct mitotic figures were seen, suggesting little activity of the tumor, which was contrary to the clinical findings of malignancy including invasion into the iris of this neoplasm. Even so, a case histologically diagnosed as a benign hemangiopericytoma resulted in death due to metastatic spread [15]. …”

Unusual occurrence of orbital hemangiopericytoma in the zygomatic bone of an adolescent: a case report

“…HPC is a rare vascular soft-tissue tumor that can develop anywhere in the body that has blood vessels, most notably in lower extremities, pelvic fossa, retroperitoneum and nasopharynx [ 5 ]. HPC rarely involves the orbit [ 6 ] and constitutes only 1.57% of orbital tumors [ 7 ]. Likewise, bones are uncommonly involved in HPC, which accounts for 4.7% of bone tumors [ 2 , 3 ].…”

“…The treatment of choice for HPC is complete en-bloc surgical excision whenever possible, because these tumors are most often circumscribed or enclosed by a pseudocapsule [ 7 , 11 ]. Completeness of surgical resection positively affects survival, while incomplete excision (piece-meal resection) or incisional biopsy are associated with local spread, recurrence and metastasis [ 7 , 11 ]. However, as in our case, complete tumor resection can occasionally be challenging due to its friable and highly-vascular nature [ 21 ].…”