Portal hypertension as a complication of idiopathic retroperitoneal fibrosis

Portal Hypertension in a Child with Retroperitoneal Fibrosis

“…Five weeks later, a second operation was attempted , and splenorenal shunt and splenectomy were performed becau se the fibrotic tissues were far less extensive on the left side . There were four other similar reports (three of esophageal varices and one of duodenal varices), but all were of adult patients (10)(11)(12)(13).…”

“…Patients with RPF may infrequently have the complication of portal hypertension caused by compre ssion of the portal venous system by thick fibrous tissue (9)(10)(11)(12)(13). Eiseman and Yeoh (9) in 1962 reported on a 13-year-old boy who developed repeated hematemesis and had splenomegaly and esophageal varices , but no evidence of cirrhosis was found .…”

“…It exerts serious complication through the compression of various abdominal tubular structures including ureters, great vessels, common bile.ducts, and the portal vein. Of these, portal hypertension is a rare complication (9)(10)(11)(12)(13). We report a 15-year-old girl with idiopathic RPF, who presented with portal hypertension as the initial manifestation; there was coexisting obstructive uropathy.…”