Pigmented Paravenous Chorioretinal Atrophy

Cheung, Dik S.

doi:10.1016/0002-9394(84)90465-3

Cited by 7 publications

(4 citation statements)

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“…Although typically quoted as being bilateral, a number of unilateral cases have been described, with lesions typically arranged in a symmetric pattern about the retinal vessels. 3 , 4 Unifocal disease, as seen in our patient, is exceedingly rare, with a single report describing unifocal disease in the mother and sister of a patient with bilateral PPRCA. 5 PPRCA holds many similarities in appearance to RP, and it has been suggested that the two diseases may lie on a continuum.…”

Section: Discussionmentioning

confidence: 61%

“…Only four cases of unilateral PPRCA have been reported in the literature. 3 , 4 , 5 Here we present an extremely rare case of unilateral and unifocal PPRCA.…”

Section: Introductionmentioning

confidence: 88%

“… 2 The etiology of PPRCA is unknown, but both primary retinal pigment epithelium (RPE) dysfunction and developmental abnormalities of the retinal vessels have been proposed. RPE dysfunction appears to be the leading theory for the cause of PPRCA owing to its severely atrophied appearance, 3 but this explanation fails to account for its characteristic peri-venular arrangement. Only four cases of unilateral PPRCA have been reported in the literature.…”

Section: Introductionmentioning

confidence: 99%

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A rare case of unifocal, unilateral pigmented paravenous retinochoroidal atrophy (PPRCA)

Ahmad

Leisy

Carr

et al. 2016

American Journal of Ophthalmology Case Reports

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PurposeTo report an atypical case of unifocal, unilateral pigmented paravenous retinochoroidal atrophy (PPRCA) characterized by thickening and cystic degeneration of the retinal nerve fiber layer (RNFL).ObservationsA 79-year old Asian woman presented with a large area of atrophic, pigmented change along the inferior arcade of her right eye. She denied nyctalopia and any other visual complaints. Visual acuity was 20/40 in both eyes and visual fields were significant for a large absolute peripheral scotoma superiorly in the affected eye corresponding to the atrophic area. Spectral domain optical coherence tomography through the lesion showed loss of choroid except for largest Haller's layer vessels, significant retinal pigment epithelium atrophy with migration and pigment clumping, outer retinal layer loss and RNFL thickening with cystic degeneration. Fundus autofluorescence imaging showed a large area of hypoautofluorescence corresponding to the area of atrophy. Full field electroretinogram demonstrated normal scotopic response and reduced photopic response in the right eye.Conclusions and importancePPRCA is typically bilateral and symmetric, affecting primarily the outer retina and choroid. However, in rare cases, this disease can present unilaterally and/or unifocally, with degeneration extending to the inner retinal layers.

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Section: Discussionmentioning

confidence: 61%

“…Only four cases of unilateral PPRCA have been reported in the literature. 3 , 4 , 5 Here we present an extremely rare case of unilateral and unifocal PPRCA.…”

Section: Introductionmentioning

confidence: 88%

Section: Introductionmentioning

confidence: 99%

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A rare case of unifocal, unilateral pigmented paravenous retinochoroidal atrophy (PPRCA)

Ahmad

Leisy

Carr

et al. 2016

American Journal of Ophthalmology Case Reports

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“…Unilateral PPRCA, as seen in our patient, is exceedingly rare. Cheung reported a patient who had unilateral PPRCA with no history of trauma or a previous inflammatory disease [ 15 ]. Bozkurt et al described a patient of PPRCA and unilateral focal atrophic lesions in his mother and sister [ 16 ].…”

Section: Discussionmentioning

confidence: 99%

Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report

Liang

Yang

et al. 2023

BMC Ophthalmol

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Background Pigmented paravenous retinochoroidal atrophy (PPRCA) is an uncommon fundus disease characterized by perivenous aggregations of pigment clumps and retinochoroidal atrophy distributed along the retinal veins. We report a Chinese female case of unilateral PPRCA with acute angle-closure glaucoma (AACG). Case presentation A 50-year-old Chinese female presented with vision loss and elevated intraocular pressure (IOP) in the right eye and then underwent trabeculectomy. She referred to our clinic for further evaluation and treatment. The funduscopic examination revealed grayish retinochoroidal atrophy and osteocyte-like pigment clumping lesions along the retinal veins and peripapillary preretinal hemorrhage in the right eye. The patient also presented with AACG in the same eye on the basis of past medical history of acute attack, shallow anterior chamber depth (ACD), narrow angle showed by ultrasound biomicroscopy (UBM) and glaucomatous neuropathy identified by optical coherence tomography (OCT). Other examinations like fluorescein fundus angiography (FFA), electroretinogram (ERG) and electrooculography (EOG) all confirmed the aforementioned diagnose. Conclusion PPRCA is a rare disease, uncommon in females and symmetrical in both eyes. We present a rare case of unilateral PPRCA accompanied with AACG.

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Cross‐flow separation of yeast cell suspensions using a sintered stainless steel filter tube

Kavanagh

Brown

1987

J of Chemical Tech & Biotech

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A new design of cross‐flow filtration unit, the Transep filter, has been investigated for the separation of slurries of Saccharomyces cerevisiae. Porous cylindrical sintered stainless steel tubes of 2 μm and 3 μm nominal pore size ratings were used as filter media. Filtration rates were measured for cell suspensions ranging from 3 to 25 kg m−3. The 3 μm filter produced particle‐free filtrates at average rates from 1.25 m3 m−2 h−1 which declined to half this value over the range of cell concentrations studied.

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Pigmented Paravenous Chorioretinal Atrophy

Cited by 7 publications

References 0 publications

A rare case of unifocal, unilateral pigmented paravenous retinochoroidal atrophy (PPRCA)

A rare case of unifocal, unilateral pigmented paravenous retinochoroidal atrophy (PPRCA)

Unilateral pigmented paravenous retinochoroidal atrophy with acute angle-closure glaucoma: a case report

Cross‐flow separation of yeast cell suspensions using a sintered stainless steel filter tube

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