Physiotherapy in the Management of Hemophilia

Beeton, Karen; Padkin, Jane

doi:10.1002/9781444318555.ch31

Cited by 4 publications

(4 citation statements)

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“…And at the time of study, most of the patients in the sample population studied were of severe type of Haemophilia, which was 52% (42.32%-61.54% at 95% confidence interval). [16][17][18][19] Functional independence score is indicating that Psychometric values of emotions are clearly related to pain and inability to move among haemophiliac patients and issues related to pain dominate the Psychological health of a patient compared to locomotion. As observed, pain in major joints (Knee, Ankle and Elbow) seemed to dominate the mobility and feeling of self-satisfaction among the sample population.…”

Section: B a C K G R O U N D Figure 2 Discussionmentioning

confidence: 99%

Functional Independence Score in Haemophilia: A Hospital Based Observational Study in a Tertiary Care Center in Central India

Choudhary¹,

Sharma²,

Nigam³

et al. 2019

jebmh

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BACKGROUND Functional Independence Score in Haemophilia (FISH) is a performance-based assessment tool, to objectively measure the patient's functional disability. The present study was done to assess the functional abilities of haemophiliac patients presenting to a tertiary care centre. METHODS This hospital based observational study was performed on all patients (100) diagnosed as haemophilia referred to Hamidia Hospital from 1 st March 2017 to 30th June 2018. Patients with other bleeding disorders and patients on medication which can alter coagulation profile were excluded. RESULTS Mean FISH for mild, moderate and severe haemophilia was 25.26±2.62, 23.65±3.67 and 21.81±2.65 and overall mean was 23.51±3.23. CONCLUSIONS The functional components like transfer and locomotion were mainly determined by joint bleeds and total joint score respectively which were observed by the positive correlation between the respective components. Hence more the bleed and joint score, higher the dependence for transfer and locomotion.

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Section: B a C K G R O U N D Figure 2 Discussionmentioning

confidence: 99%

Functional Independence Score in Haemophilia: A Hospital Based Observational Study in a Tertiary Care Center in Central India

Choudhary¹,

Sharma²,

Nigam³

et al. 2019

jebmh

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“…Over 70% of the patients with severe or moderate hemophilia were trained to perform home treatment, indicating good coverage by the program which periodically seeks to add new patients and families. At the time of the study, physical therapy had not yet been incorporated as routine care provided to patients with hemophilia, even though it is considered essential in the rehabilitation of these individuals ( 25 ) .…”

Section: Discussionmentioning

confidence: 99%

Health-related quality of life in hemophilia: results of the hemophilia-Specific quality of life index (Haem-a-Qol) at a Brazilian blood center

Ferreira¹,

Leite²,

Bustamante-Teixeira³

et al. 2013

Revista Brasileira De Hematologia E Hemoterapia

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BackgroundStudies on health-related quality of life are based on the increasingly evident need for medical care not to be limited to preventing death, but to focus instead on the value of health. ObjectiveThis study aimed to measure the health-related quality of life in hemophilia, using the Hemophilia- Specific Quality of Life (Haem-A-QoL) questionnaire and describe the socioeconomic characteristics and health conditions of these patients. MethodsThe Brazilian version of the Hemophilia-Specific Quality of Life questionnaire was administered to hemophiliac adults, treated in an on-demand regime at the Juiz de Fora Regional Blood Center - HEMOMINAS Foundation. The patients were interviewed about demographic and socioeconomic data and their understanding of the questionnaire. Clinical data were collected from medical records. The Mann-Whitney U test was used for statistical analysis. The level of significance was set for p-values < 0.05. Statistical analysis was performed using the Statistical Package for the Social Sciences (SPSS, version 15.0). ResultsThirty-nine patients were evaluated. The mean age was 36.8 years. 84.6% had hemophilia A; 20.5% of the patients had hemophilia classified as mild, 41% as moderate and 38.5% as severe. The records of 10.5% of the patients registered seropositivity for anti-HIV and 57.9% for anti-HCV. Target joints were detected in 69.2%. The mean total Hemophilia-Specific Quality of Life score was 35.55. 'Sports and leisure'and 'Physical health'were the most impaired dimensions and the dimension 'Relationship and partners'was the least impaired. The Hemophilia-Specific Quality of Life scores showed good discriminant validity for hemophilia severity (p-value = 0.001), HIV-infection (p-value = 0.02), HCV-infection (p-value = 0.01) and the presence of target joints (p-value < 0.001). ConclusionHealth-related quality of life in hemophilia, measured by the Hemophilia-Specific Quality of Life questionnaire, was influenced by the presence of arthropathy and infectious diseases transmitted by blood products. Rehabilitation measures should be encouraged in order to improve the quality of life of these patients.

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“…Over 30% reported not having access to physiotherapy followup, 34 even though physiotherapy is considered essential for the treatment and rehabilitation of patients with hemophilia. 35 …”

Section: Comprehensive Health Care and Hemophilia A In Brazilmentioning

confidence: 99%

Hemophilia A in Brazil – epidemiology and treatment developments

Ferreira¹,

Leite²,

Bustamante-Teixeira³

et al. 2014

JBM

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Hemophilia A is an inherited disorder characterized by deficiency of coagulation factor VIII, which predisposes patients to bleeding events. Treatment is based on replacement of the deficient factor, in a therapeutic or prophylactic manner. Brazil is the country with the third largest population of people with hemophilia, for which the public health system provides free comprehensive care. Maintaining an updated registry of patients, documenting the prevalence of complications, and assessing the effectiveness of resource use are indispensable elements in the design of a well-coordinated national program. According to sociodemographic, clinical, and laboratory data collected by the computerized Brazilian system on coagulopathies, in June 2013, there were 9,122 registered patients with hemophilia A in Brazil, of which 36.1% had a severe form of the disease. Clotting factor inhibitors were present in 7.5%, but 25.7% of records did not provide this type of data. Around 70% of the patients belonged to the economically active population, being between 15 and 59 years old. Infection by the human immunodeficiency virus was present in 23.4% of the patients tested and infection by hepatitis C virus antibodies in 59.3%. Infection by the hepatitis B virus and human T-lymphotropic virus was also reported. The high percentage of incomplete records regarding serological data shows the fragility of the information system to date. There was also no information available on the prevalence of permanent or disabling joint damage. Although few hemophiliacs receive adequate care in developing countries, and despite Brazil exhibiting great social inequalities, the Ministry of Health has made significant advances in the treatment of hemophilia A. The gradual increase in importation of factor VIII concentrate enabled the implementation of primary and secondary modalities of prophylaxis, in addition to the induction of immune tolerance. There are also plans to set up a factory in the country, to ensure Brazilian self-sufficiency in the production of blood products.

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Physiotherapy in the Management of Hemophilia

Cited by 4 publications

References 46 publications

Functional Independence Score in Haemophilia: A Hospital Based Observational Study in a Tertiary Care Center in Central India

Functional Independence Score in Haemophilia: A Hospital Based Observational Study in a Tertiary Care Center in Central India

Health-related quality of life in hemophilia: results of the hemophilia-Specific quality of life index (Haem-a-Qol) at a Brazilian blood center

Hemophilia A in Brazil – epidemiology and treatment developments

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Physiotherapy in the Management of Hemophilia

Cited by 4 publications

References 46 publications

Functional Independence Score in Haemophilia: A Hospital Based Observational Study in a Tertiary Care Center in Central India

Functional Independence Score in Haemophilia: A Hospital Based Observational Study in a Tertiary Care Center in Central India

Health-related quality of life in hemophilia: results of the hemophilia-Specific quality of life index (Haem-a-Qol) at a Brazilian blood center

Hemophilia A in Brazil &ndash; epidemiology and treatment developments

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Hemophilia A in Brazil – epidemiology and treatment developments