Pathergic Granulomatosis

Sternberg, Thomas H.; Reynolds, John V.; Zeilenga, Robert H.

doi:10.1001/archderm.1957.01550150054005

Cited by 11 publications

(1 citation statement)

References 8 publications

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“…The concept of limited Wegener's granulomatosis has been confirmed by others (Israel & Patchefsky 1971;Novack & Pearson, 1971;Cassan, Coles & Harrison, 1970;Fauci & Wolff, 1973). This condition is probably the same as the cases which were described as idiopneumonic necrotizing granulomatosis (Fienberg, 1953), pathergic granulomatosis (Fienberg, 1955;Hood, O'Connell & McCord, 1958) and necrotizing granuloma of the lung (Lansdown, 1961). More recently it has been shown that glomerulonephritis may occur in limited Wegener's granulomatosis (Horn et al, 1974).…”

Section: Discussionmentioning

confidence: 63%

Lymphomatoid granulomatosis

Macdonald¹,

Sárkány

1976

Clin Exp Dermatol

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Summary Two cases of lymphomatoid granulomatosis are described. The clinical features included pruritus, acquired ichthyosis, widespread skin nodules and plaques, skin ulceration, patchy alopecia and loss of sweating. Skin biopsies showed lymphomatous and granulomatous changes associated with a vasculitis. In one patient chest radiographs revealed several shadows in the lower zones of the lung fields. His disease improved on treatment with systemic steroids both alone and in combination with cyclophosphamide. The second patient's condition later evolved into Hodgkin's disease, which responded to treatment with cytotoxic drugs. Both patients eventually died of pneumonia possibly related to their therapy.

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