Paediatric paramenigeal rhabdomyosarcoma: a case report – multimodal treatment

Minimally Invasive Approach for Orbital and Parameningeal Rhabdomyosarcoma

“…Parameningeal sites account for 41%-51,2% of head and neck RMS. It has been reported only few cases arising in the paranasal sinuses and orbit like our patient [10,19]. Torres-Peña y cols presented two male adults (24 and 26 years respectively) with anterior cranial base alveolar RMS with orbital extension [20].…”

“…Soft tissue sarcoma of the head and neck in an adult patient is very rare with only several cases reported in literature [1,2,[6][7][8][9][10]. RMS is a rare and aggressive malignancy first described in 1854 by Weber and colleagues possibly originating from primitive mesenchymal cells that arise anywhere in the body, including sites where striate muscle is not found like nasal cavity and paranasal sinuses which represent only 10% of soft tissue sarcomas and less than 1% of malignant nasosinusal tumors in adults [11,12].…”

Pediatric Sinonasal Rhabdomyosarcoma Presented as Squint: A Case Report and Literature Review

“…We reviewed nine cases of confirmed sinonasal RMS from 2003 until 2017. The pleomorphic subtype was seen only in one case, whilst the rest were embryonal [4][5][6][7][8][9][10]. We summarized the findings of the previous cases together with the present case in Table 1.…”

“…Two patients had an ocular complaint as the presenting symptom; one case presented with sudden onset reduced vision, while the other had unilateral protrusion without visual disturbances [ 4 , 5 ]. There was one case in which the parents denied any ocular symptoms but noted the patient to have mild proptosis during the initial assessment [ 6 ]. Our patient differs from other cases whereby this patient developed acute onset squint followed by rapid proptosis and blurred vision without anteceding nasal symptoms.…”