Orbital Myositis in Churg-Strauss Syndrome

Paranasal sinus inflammation and non-specific orbital inflammatory syndrome: an uncommon association

“…The most common specific systemic granulomatous inflammations that are known to affect the paranasal sinuses and orbits are Wegener's granulomatosis, sarcoidosis, and Churg-Strauss syndrome [2,5,14,15]. The lack of obvious renal or pulmonary involvement in all our patients, the negative serology (ANCA and ACE) and the absence of granulomas on histopathology makes the diagnosis of Wegener's granulomatosis or sarcoidosis less likely.…”

Painful Ophthalmoplegia as Ocular Manifestation in Cytophagic Histiocytic Panniculitis Associated with Churg Strauss Syndrome

“…Several orbital inflammatory pseudotumors or, more precisely, idiopathic orbital inflammation have been reported associated with CSS (Billing et al, 2004), but, to our knowledge, none with exophthalmia and ophthalmoplegia.…”

Bilateral Subconjunctival Masses as a Rare Presentation of Churg-Strauss Syndrome

“…No formal diagnosis of CSS had been made in this patient until the histological confirmation. The remaining cases cited in the literature all had unilateral involvement [10][11][12][13][14][15] with either a single nodular elevation of the conjunctiva, [10][11][12] progressive thickening of the bulbar and palpebral conjunctiva, 13 or a nodular infiltration of the tarsal conjunctiva causing a fullness 14 and an irregular consistency of the upper eyelids. 15 However, the nodular tarsal conjunctival lesions in this last case also showed amyloid deposits and were similar in appearance to that in other reported cases of conjunctival amyloidosis.…”