Orbital Melanocytoma

Abstract

Recurrent intermediate grade orbital melanocytomas are rarely encountered and have to be distinguished from other topographically similar primary melanotic tumors. They have to be managed more aggressively if intracranial extension is present due to its close relation to the visual pathways.

Intermediate-grade meningeal melanocytoma associated with nevus of Ota

“…Of PMMTs, the IGMs constitute a small percentage with only 13 previously reported cases [7,15,[40][41][42][43][44][45][46][47][48][49][50]. Of PMMTs, the IGMs constitute a small percentage with only 13 previously reported cases [7,15,[40][41][42][43][44][45][46][47][48][49][50].…”

Orbital melanocytoma completely resected with conservative surgery in association with ipsilateral nevus of Ota: Report of a case and review of the literature

“…To the best of our knowledge, there are only 4 described cases of orbital melanocytomas and 1 case of meningeal sphenoid melanocytoma with frontal white matter extension and 2 associated retrobulbar lesions . Including the present report, all the isolated orbital cases occurred in the right orbit of adult men, with ages ranging from 28 to 51 years old.…”

“…Intraocular melanocytomas can also occur, involving the iris, choroid, and ciliary body . Approximately 110 cases of meningeal melanocytomas have been reported in the literature, whereas orbital melanocytomas have been rarely reported …”

“…Three patients underwent total resection without any adjuvant therapy. One patient was submitted to subtotal excision and received chemotherapy alone, whereas 1 patient was treated with subtotal excision and received radiotherapy associated with chemotherapy . All 5 patients were alive without evidence of disease, with the follow‐up time ranging from 6 months to 12 years.…”

Tumores primários da órbita incomuns diagnosticados por biópsia com agulha grossa guiada por tomografia computadorizada: relato de dois casos

“…It is important to differentiate primary melanocytic lesions from those of metastatic origin, considering that they require different therapeutic approaches. The absence of a known malignant melanoma is useful in the differentiation of such tumors, and a complete investigation of these patients is essential in the search for a diagnosis (5,6) .…”