Morphea Associated With Hemiatrophy of the Face

Osborne, Earl D.

doi:10.1001/archderm.1922.02360010030005

Cited by 10 publications

(2 citation statements)

References 2 publications

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“…Archambault and Fromm evoked trigeminal peripheral neuritis [41,49,51], cervical sympathetic loss [2,10,18], cephalic trophoneurosis [74], and scleroderma [13,14,39,63]. Only the latter two seem still valid.…”

Section: Heredodegenerative Hypothesismentioning

confidence: 99%

Progressive hemifacial atrophy: historical review and actual features related to a new classification of facial hypoplasia and atrophy

et al. 1994

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progressive hemifacial atrophy, described initially by Parry and Romberg, is reviewed in terms of etiopathogenesis and clinical features. The purpose is to clarify the variegated nature of this syndrome and to distinguish it from other forms of atrophy affecting the face, principally the soft tissues. The authors propose a new general classification of hypoplasia and atrophy of the face.Progressive hemifacial atrophy (PHA) is an acquired syndrome affecting peculiarly the subcutaneous fatty tissue together with skin, mimic musculature, bone and cartilage in that order of frequency. The etiology is unknown but neurodystrophic and sclerodermic theories have been suggested. The incidence in the population is at present unknown. Female/male ratio is 3 : 2 according to Rogers, while Archambault and Fromm, Mussinelli et al. and Rees reported ratios less than 1.2:1. Other authors, mainly in early papers, reported a very high occurrence in women [2,56,71,73]. Nerobyeyev et al., in 1990, noted a ratio higher than 4:1 [59]. The left side of the face is not significantly more affected than the right side; bilateral incidence is almost 5% [56, 72], but according to Rees bilateral involvement in Scleroderma or Romberg's atrophy is "'more unique than rare" [71]. The disease starts in the first or second decade of life (mean age: 5 15 yrs. ; range of 1-70 yrs.); and progresses slowly for 2-10 yrs. with long periods of remission. HistoryThe clinical features were described by Parry and Romberg [64,74]. It was called "progressive facial hemiCorrespondence to .' Dr. R. Roddi,

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Section: Heredodegenerative Hypothesismentioning

confidence: 99%

Progressive hemifacial atrophy: historical review and actual features related to a new classification of facial hypoplasia and atrophy

et al. 1994

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“…The reported (1959) Cerebellar atrophy, Purkinje cell loss 1 This report pathological changes in facial hemiatrophy have been varied. Biopsy findings from affected face and limbs have revealed inconstant osteoporosis, inflammation, fibrosis, and vasculitis in the subcutaneous fat and deep layers of the skin (Osborne, 1922;Hickman and Sheils, 1964;Ashley et al, 1965). Such changes have been variously interpreted and in one patient (Hickman and Sheils, 1964) were suggestive of dermatomyositis.…”

Section: Discussionmentioning

confidence: 99%