Management of an infant with epidermolysis bullosa on invasive mechanical ventilation

Abstract

Objective: To describe, for the first time in the pediatric population, the use of an effective technique to mobilize secretion in a patient whose disease imposes many care limitations. Case description: 2-year-old infant with Epidermolysis Bullosa, dependent on mechanical ventilation after cardiorespiratory arrest. Infant evolved with atelectasis in the right upper lobe with restriction to all manual secretion mobilization techniques due to the risk of worsening skin lesions. We opted for tracheal aspiration in a closed system combined with expiratory pause, a technique only described in adult patients so far. Comments: This case report is the first to use this technique in a pediatric patient. The use of expiratory pause combined with tracheal aspiration not only optimized the mobilization of secretion, but it was also a safe tool for reversing atelectasis. Our case report brings an important result because it increases the possibilities of managing pediatric patients admitted to intensive care units, especially in situations of absolute contraindication for chest maneuvers.

Development and validation of educational hypermedia for family members and caregivers of people with epidermolysis bullosa

“…There are 994 individuals registered with EB currently in the country and, 147 of these have evolved to death so far. Of the total registered, there are 406 living people aged between 0 and 15 years (3) .…”

Desenvolvimento e validação de hipermídia educativa para familiares e cuidadores de pessoas com epidermólise bolhosa

“…No país, há 994 indivíduos cadastrados com EB atualmente e, destes, 147 evoluíram para óbito até o momento. Do total de cadastrados, há 406 vivos com idade entre 0 e 15 anos (3) .…”