Left Pulmonary Artery from the Ascending Aorta: A Case Report and Review of Published Cases

Loomba, Rohit S.; Aiello, Salvatore; Tretter, Justin T.; Gaffar, Maira; Reppucci, Jennifer; Brock, Michael; Spicer, Diane E.; Anderson, Robert H.

doi:10.3390/jcdd8010001

Cited by 4 publications

(4 citation statements)

References 83 publications

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“…CT angiography (CTA) has a unique advantage in displaying the abnormal course and spatial orientation of the peripheral blood vessels of the heart and arterial system, it can show that the beginning of the pulmonary artery branch on the affected side is the blind end [4][5][6][7]. But it has some limitations in the direction of blood flow, and radiation, which is difficult to tolerate in children and the development of screening is limited [8]. Conventional pulmonary angiography is the "gold standard" for imaging diagnosis of this disease, which can reflect the absence of pulmonary artery length and collateral vessels.…”

Section: Introductionmentioning

confidence: 99%

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Tian¹,

Zheng²

2021

Reviews in Cardiovascular Medicine

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The unilateral absence of pulmonary artery (UAPA) is a rare congenital cardiovascular malformation, which is asymptomatic and easy to be ignored in early stage. A large number of complications may occur in the later stage. Therefore, early diagnosis and treatment is of great significance. The imaging data of 49 patients with UAPA discovered and confirmed clinically by the echocardiography in our hospital are analyzed. The results show that left pulmonary artery absence is more common (55%) and most of them are associated with other cardiovascular malformations (92%). Atrial septal defect and patent foramen ovale were most common in 56%. In which the absence of isolated pulmonary artery was 8% (4/49), and the absence of right pulmonary artery was 75% (3/4). Especially in the patients with tetralogy of Fallot, 77% (5/9) of them miss the diagnosis of UAPA. This suggests that doctors and sonographers should pay attention to the development of pulmonary artery bifurcation and left and right branches in multi-section, and strengthen the scanning of short axis section of high large artery.

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Section: Introductionmentioning

confidence: 99%

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Tian¹,

Zheng²

2021

Reviews in Cardiovascular Medicine

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“…According to an article by Loomba et al, out of 113 patients with anomalous LPA arising from the ascending aorta, the most common associated cardiac abnormality was TOF, which was seen in 59 cases (52.2% of the total) [ 9 , 10 ]. In a study of 216 patients diagnosed with TOF, it was noted that 38.9% of them had pulmonary artery abnormalities, with isolated LPA stenosis being the most common [ 11 ].…”

Section: Discussionmentioning

confidence: 99%

An Unusual Relation in an Infant With Left Hemitruncus and Tetralogy of Fallot Along With Pulmonary Valve Syndrome: A Case Report

Ghosh,

Sahai,

Raut

et al. 2024

Cureus

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The abnormal origin of the left pulmonary artery (LPA) from the ascending aorta is a rare cardiac condition that is often associated with several other congenital defects. In this paper, we report the case of an infant who presented with recurrent infections and was prenatally diagnosed with tetralogy of Fallot (TOF). During echocardiography, various other cardiac defects such as ventricular septal defects (VSD), pulmonary stenosis (PS), and dilated right heart chambers were identified. Furthermore, cardiac catheterization revealed an anomalous origin of the LPA arising from the aorta associated with a narrow pulmonary annulus. Due to both conditions sharing a similar embryological course, the condition is commonly associated with a conotruncal defect known as DiGeorge syndrome. Together, the overall combination of cardiac anomalies is both unusual and unique. This case study explains the clinical associations, embryological origin, and surgical management of this condition in an infant.

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“…It can occur with tetralogy of Fallot and aortic arch anomalies. 3,4 Anomalous origin of left pulmonary artery results in a significant left-to-right shunt and burdens the right lung with the entire right ventricular output and subjects the left lung to systemic pressure, posing a risk for development of pulmonary vascular disease.…”

Section: Introductionmentioning

confidence: 99%

Hypoplastic Circumflex Aorta With Anomalous Left Pulmonary Artery: Uncrossing Operation in a Neonate

Alloah,

Misra,

Kwon

et al. 2024

World J Pediatr Congenit Heart Surg

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Circumflex aortic arch with coarctation and anomalous origin of the left pulmonary artery from the aorta are rare cardiovascular anomalies. These conditions can lead to early pulmonary hypertension and challenging management. Early diagnosis and surgical intervention are beneficial for optimal outcome. We present a case where both anomalies coexisted and were repaired with aortic uncrossing, arch augmentation, and reimplantation of the left pulmonary artery. To our knowledge, this is the first documented instance of these anomalies coexisting and being repaired in the neonatal period.

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Left Pulmonary Artery from the Ascending Aorta: A Case Report and Review of Published Cases

Cited by 4 publications

References 83 publications

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

Unilateral absence of pulmonary artery analysis based on echocardiographic feature

An Unusual Relation in an Infant With Left Hemitruncus and Tetralogy of Fallot Along With Pulmonary Valve Syndrome: A Case Report

Hypoplastic Circumflex Aorta With Anomalous Left Pulmonary Artery: Uncrossing Operation in a Neonate

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