volume 89, issue 1, P26-36 2014
DOI: 10.1590/abd1806-4841.20142584
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Claudia Schermann Poziomczyk,
Julia Kanaan Recuero,
Luana Bringhenti
et al.

Abstract: Incontinentia pigmenti is a rare genodermatosis in which the skin involvement occurs in all patients. Additionally, other ectodermal tissues may be affected, such as the central nervous system, eyes, hair, nails and teeth. The disease has a X-linked dominant inheritance pattern and is usually lethal to male fetuses. The dermatological findings occur in four successive phases, following the lines of Blaschko: First phase - vesicles on an erythematous base; second phase - verrucous hyperkeratotic lesions; third …

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