Imagerie multi-modale d’une fermeture de l’angle liée à une sphérophaquie dans un syndrome de Weill-Marchesani

In vitro biometry of a human spherophakia

“…A steep anterior lenticular curvature has been noted in OCT and ultrasonic biomicroscopic studies of spherophakia. 10,17–19 The small difference between the anterior and posterior curvature observed in our study may be a distinguishing feature of spherophakia. These changes in curvature present typically as lenticular myopia.…”

“…20 Such a heavy lens is more prone to dislocation or subluxation, leading to ectopia lentis and/or pupillary block. 19 Hence, it is not only the size but also the weight of the lens in spherophakia that may predispose the eye to secondary glaucoma.…”