Idiopathic Atrophoderma of Pasini and Pierini with Coexistent Morphea

Atrophoderma of Pasini and Pierini: a clinical and histopathological study

“…Second, morphea‐like induration within atrophoderma lesions has been repeatedly described 3,4,7 . Third, classical morphea plaques may co‐occur with IAPP in the same patient 4,6,11,15 . Fourth, progression from IAPP to systemic scleroderma was described in one patient 24 .…”

“…The elastic tissue stain of lesional skin is essentially normal 3,4,7,10 . However, few reports have found a decreased amount of elastic fibers in the dermis 4,9,14,15 . Direct immunofluorescence may be negative 6 or non‐specific 8 .…”

Atrophic wrinkled plaque on face: a diagnostic dilemma

“…Also, the site of the lesion (face) is perplexing as face, hand and feet are invariably spared in atrophoderma and rarely involved in elastolytic disorders. 6 The lesion on the contralateral cheek, unnoticed by the parents, probably represents the early stage of the disease pathogenesis.…”