Iatrogenic Supravalvular Aortic Stenosis Detected by Transesophageal Echocardiography in a Pediatric Patient Undergoing Cardiac Surgery

Lee, Ji‐Hyun; Nam, Karam; Park, Yong‐Hee; Kim, Jin‐Tae

doi:10.1213/ane.0000000000000486

Cited by 1 publication

(1 citation statement)

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“…Congenital supravalvular aortic stenosis (SAS), characterized by congenital narrow of the ascending aorta, occurs sporadically and has an incidence of 1 in 20000 newborns [1]. Etiology is still obscure while various factors make contributes to SVAS such as genetic abnormalities including ELN gene [2], vitamin metabolism deficiency [3] and iatrogenic causes [4,5]. In 1961, Williams [6] firstly described the characteristics of congenital SAS such as mental retardation, macroscopic features which appears to originate from soft-tissue similarities while with little business of skulls, tortuous retinal vessels, lower weight for ages and the likes.…”

Section: Introductionmentioning

confidence: 99%

TEE Provided Advantageous Information for a Surgical Resolution of Obstruction of SAS Suffering Difficulty in Removing CPB: A Case Report

Lin¹,

Chen

Zhou

et al. 2019

BJSTR

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Congenital heart disease (CHD) is the most common type of congenital malformations. Congenital supravalvular aortic stenosis (SAS), one kind of CHDs, is strongly associated with abnormal aortic sac development with low prevalence while shows considerable impacts on infants' physical and mental development. Presently, surgical treatment is an effective therapy for SAS with acceptable surgical risk and good late survival. Evaluating the stenosis grade preoperative, the real-time status of heart during surgical correction are extremely crucial. Transesophageal echocardiography (TEE), has the advantages of clear images without interference of surgical field, is widely applied in diagnosis of cardiovascular diseases and intraoperative continuously monitoring. Here, we presented a successful case of surgical resolution of obstruction of congenital SAS in an infant who suffered difficulties in removing cardiopulmonary bypass (CPB) under the guidance of TEE.

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