Evaluation and Treatment of Congenital Facial Paralysis

Nervus Intermedius Guides Auditory Brainstem Implant Surgery in Children with Cochlear Nerve Deficiency

“…4 This hypothesis is also supported by clinical observations in the present study and reports in the literature that children with unilateral congenital facial palsy do not exhibit abnormalities of the somatosensory and parasympathetic function of the NI. 41-43…”

“…A number of factors suggest that the NI is not part of cn VII but rather a distinct nerve—that is, the variable number and different origins of the NI bundles; the outcome of embryologic and comparative studies disclosing different mechanisms in the embryogenesis of the NI with respect to cn VII in humans, cats, and white rats 40 ; and evidence that electrical stimulation of the NI in the CPA evokes a selective motor response in the area of the perioral muscles, clearly distinct in morphology, amplitude, and latency from motor responses of the facial nerve 4 . This hypothesis is also supported by clinical observations in the present study and reports in the literature that children with unilateral congenital facial palsy do not exhibit abnormalities of the somatosensory and parasympathetic function of the NI 41‐43 …”

Non-traumatic congenital facial nerve paralysis; electroneurophysiologic evaluation of four cases

“…They further interpreted this finding as the motor portion of the nerve should have developed much later than the sensory portion [18]. Harris et al explored the facial nerve in a 14-year-old girl with congenital facial paralysis and found atretic nerve below the take off of the chorda tympani [11]. Therefore, sensorial function can be intact despite motor impairment of the facial nerve.…”

“…Prolongation of interpeak wave latencies and decrease in amplitude of the waves at the involved side in those patients with congenital facial nerve paralysis is an important finding although the hearing is normal [11,20,24,26]. Erro et al reported a 13-year-old boy with congenital facial diplegia and prolongation of I-V interpeak latencies on both sides whose his family was affected over four generations [7].…”

Eighth Nerve Aplasia and Hypoplasia in Cochlear Implant Candidates: The Clinical Perspective

“…Möbius syndrome consists of congenital facial palsy without a history of birth trauma (18) and can be associated with dysfunction of other cranial nerves as well as with orofacial and limb malformations, defects of the musculoskeletal system, and mental retardation (19). To our knowledge, there are no reports of the prevalence of absence of the eighth nerve in CHARGE syndrome; however, the IAM has been reported to be narrow in 2 of 50 (16) and up to 1 of 10 (17) patients with CHARGE syndrome.…”