1974
DOI: 10.1001/archderm.110.6.894
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Epidermolysis bullosa dystrophica with epidermal neoplasms

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Cited by 35 publications
(39 citation statements)
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“…Since the first reported case in 1913, cutaneous SCC in EB remains the most devastating and fearful complication with a high morbidity and mortality (6,7). The risk of developing SCC begins to increase at adolescence and is the highest in recessive dystrophic EB (RDEB).…”
Section: What Is Known About Squamous Cell Carcinoma In Epidermolysismentioning
confidence: 99%
“…Since the first reported case in 1913, cutaneous SCC in EB remains the most devastating and fearful complication with a high morbidity and mortality (6,7). The risk of developing SCC begins to increase at adolescence and is the highest in recessive dystrophic EB (RDEB).…”
Section: What Is Known About Squamous Cell Carcinoma In Epidermolysismentioning
confidence: 99%
“…4,5,7,9,18,22,28,30,36,41 (Image 24) Ankyloglossia. Ankyloglossia presumably secondary to ulceration is common, indeed may affect all patients (Image 25) 1,4,5,7,12,16,18,19,22,23,28,31,77 .…”
Section: Generalized Rdebmentioning
confidence: 99%
“…Progressive 5,78 microstomia affects almost all patients with generalized RDEB (Image 27) 1,[4][5][6][7]11,12,16,18,19,22,27,28,36,41,45,51,77 . Microstomia is not unique to generalized RDEB, and it might also be present less severely in RDBE inversa and Herlitz subtype of JEB 5,19 .…”
Section: Generalized Rdebmentioning
confidence: 99%
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“…38 In dystrophic EB, especially in severe generalized dystrophic EB of Hallopeau-Siemens, the development of malignant tumors is a well-known complication. [39][40][41] Almost all tumors occurring in this condition are SCCs [40][41][42][43][44] that most often appear on the extremities and mucous membranes of the mouth, the tongue, and the upper gastrointestinal tract. 40,41 Most SCCs complicating dystrophic EB show a propensity for metastatic spread and tumor progression, and their existence carries a grave prognosis.…”
Section: Commentmentioning
confidence: 99%