Endolymphatic sac papillary tumor: A case report and review

Yılmaz, İsmail; Bolat, Fılız; Demirhan, Beyhan; Aydin, M. Volkan; Özlüoğlu, Levent N.

doi:10.1016/j.anl.2007.06.009

Cited by 16 publications

(34 citation statements)

References 19 publications

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“…[5] The common presentation is progressive or Other clinical features include headache, dizziness, tinnitus, vertigo, cranial nerve paralysis, Vernet's syndrome, and cerebellopontine angle syndrome. [6,7] The differential diagnosis include other lesions in the cerebellopontine angle, such as, schwannoma, meningioma, jugular paraganglioma, metastatic adenocarcinoma, and choroid plexus papilloma. Early diagnosis and treatment is important in order to preserve hearing and facial nerve function.…”

Section: Discussionmentioning

confidence: 99%

“…[15,16] Surgical approaches include the transmastoid, retromastoid or retrolabyrinthine-transdural approaches, which are selected on the basis of the location and extent of the tumor and the patient's preoperative functional deficits. [6,8] The role of radiotherapy or gamma knife radiosurgery is controversial, and the published series are too few to provide a definite conclusion. Most studies reported an uncertain effect of radiotherapy or gamma knife radiosurgery.…”

Section: Discussionmentioning

confidence: 99%

“…Most studies reported an uncertain effect of radiotherapy or gamma knife radiosurgery. [6,7,9,12,17] Two cases treated with gamma knife radiotherapy, with long-term follow-up, and with no recurrence, have been reported. [5,18] In our case, the patient had only sensorineural hypoacusis and facial paresis at the time of the first admission.…”

Section: Discussionmentioning

confidence: 99%

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Gamma knife treatment of an endolymphatic sac tumor: Unique features of a case and review of the literature

et al. 2011

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

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Gamma knife treatment of an endolymphatic sac tumor: Unique features of a case and review of the literature

et al. 2011

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“…1) [38][39][40][41]. Magnetic resonance imaging (MRI) usually reveals a heterogeneous mass which is hyperintense on contrast enhanced T1 and T2 sequences due to hypervascularity [38,42].…”

Section: Clinical and Radiographic Featuresmentioning

confidence: 99%

Current Treatment of Endolymphatic Sac Tumor of the Temporal Bone

et al. 2018

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An endolymphatic sac tumor (ELST) is a rare, indolent but locally aggressive tumor arising in the posterior petrous ridge. Patients present with sensorineural hearing loss and tinnitus. As the tumor progresses, patients may experience vertigo, ataxia, facial nerve paresis, pain and otorrhea. Most patients present in their 4th or 5th decade with a wide age range. Patients with von Hippel-Lindau disease have an increased likelihood of developing ELST. Histologically, ELST is a low-grade adenocarcinoma. As it progresses, it destroys bone and extends into adjacent tissues. The likelihood of regional or distant metastases is remote. The optimal treatment is resection with negative margins. Patients with positive margins, gross residual disease, or unresectable tumor are treated with radiotherapy or radiosurgery. Late recurrences are common, so long follow-up is necessary to assess efficacy. The likelihood of cure depends on tumor extent and is probably in the range of 50-75%.

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“…[ 21 ] Although total surgical resection is the treatment of choice, it is not always feasible which can lead to post-operative recurrence. [ 9 11 26 ] Fractionated radiotherapy and stereotactic radiosurgery have been reported as treatment options in a limited number of cases.…”

Section: Introductionmentioning

confidence: 99%

Gamma knife radiosurgery in the management of endolymphatic sac tumors

Sinclair¹,

Al-Saffar²,

Brigui³

et al. 2018

Surg Neurol Int

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Background:Although widely regarded as rare epithelial tumors with a low grade of malignancy, endolymphatic sac tumors (ELST) often lead to disabling petrous bone destruction and significantly impairing symptoms at the time of primary diagnosis and/or recurrence. ELST is not uncommon in von Hippel Lindau (VHL) patients. Although open surgery is regarded as the best treatment option, recurrence remains a challenge, particularly when gross tumor resection (GTR) is deemed unachievable due to topographic conditions. Tumor recurrence successfully treated with fractionated radiotherapy and radiosurgery have been reported in selected cases. We present the case of a patient with recurrent ELST treated with salvage gamma knife radiosurgery (GKRS) adding a review of current literature.Case Description:A 65-year-old patient underwent GKRS of an unresectable, recurrent ELST. Tumor volumetric analysis showed almost 15% increase in tumor volume in the 4 months between the pre-GKRS magnetic resonance imaging (MRI) and the stereotactic MRI (s-MRI) at treatment. Follow-up MRI at 12 and 20 months showed significant decrease in local tumor volume, decreased contrast enhancement and no perifocal edema. The patient's general and neurological status remains stable to the present day.Conclusion:In the present case, GKRS was effective in the management of a recurrent ELST over the course of 20 months. Because of ELSTs recurrence potential, long-term follow up is required. The present case as well as previous reports might suggest a possible salvage/adjunctive role of radiosurgery in the management of ELST. Further studies are deemed necessary.

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Endolymphatic sac papillary tumor: A case report and review

Cited by 16 publications

References 19 publications

Gamma knife treatment of an endolymphatic sac tumor: Unique features of a case and review of the literature

Gamma knife treatment of an endolymphatic sac tumor: Unique features of a case and review of the literature

Current Treatment of Endolymphatic Sac Tumor of the Temporal Bone

Gamma knife radiosurgery in the management of endolymphatic sac tumors

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