Efficacy of a Nonrestricted Fat Diet in Patients With Cystic Fibrosis

Relation between insulin-like growth factor-I, body mass index, and clinical status in cystic fibrosis

“…Weight gain is of enormous importance to the overall prognosis in cystic fibrosis as body mass index correlates inversely with overall survival,46 and nutritional status influences the course of the disease 47. It is interesting in this respect that we observed significant correlations not only between IGF-I status and body mass index but also with the more general Shwachman score and FEV 1 .…”

Energy metabolism in cystic fibrosis

“…In planning nutritional strategies, with a view to normalizing growth and nutritional status as early as possible after diagnosis, the extra daily requirements for both energy and protein will depend both on the initial deficits and on the achievable rate of rehabilitation, preferably by non-invasive methods. It has been shown that energy intake can be enhanced and weight gain sustained for at least 4 years in CF patients using a 'normal' diet in large amounts (Luder et al 1989). There is no single optimal supplement for use in CF patients.…”

Seguimento nutricional de pacientes com fibrose cística: papel do aconselhamento nutricional

“…Although the 24-hour dietary recall has been recommended, at least annually, in the routine nutritional assessment of CF patients, 10 combining this 24-hour recall with a 3-day food record may provide a more valid assessment of an individual s intake. 14 Many nutrition interventions aimed at improving the nutritional status of CF patients have proved to be equally effective. 16 An increase in energy and fat intake and an improvement in weight in CF patients can be achieved by long-term nutrition intervention, performed by nutritional counseling.…”