Eccrine syringofibroadenomatosis (Mascaro) with mucous involvement

Recalcitrant erosive plaques on the palms and soles: A rare manifestation of eccrine syringofibroadenoma

“…In these reports, the lesions were primarily described as hyperkeratotic papules and plaques. [2][3][4][5][6] Our case represents a unique clinical manifestation of syringofibroadenomatosis characterized by progressive erosive palmoplantar plaques.…”

“…Multiple ESFA, also known as eccrine syringofibroadenomatosis , is an unusual variant of ESFA that has been primarily described in reported cases as palmoplantar hyperkeratosis. 2 , 3 , 4 , 5 , 6 Because of its rarity, ESFA is not often recognized and may be difficult to distinguish from more common inflammatory dermatoses, which may lead to inappropriate therapeutic interventions. We present a rare manifestation of ESFA that presented as progressive erosive plaques on the palms and soles of an elderly woman, which had been unresponsive to several therapies.…”

Contribución al estudio de las modificaciones de las glándulas ecrinas en relación con las neoplasias cutáneas

“…Y por otra, lesiones múltiples (nevus acrosiringial, siringofibroadenomatosis), "nevoides", con un patrón sistematizado de distribución, de aparición aislada (46,(49)(50)(51)(52)(53)(54) o en el contexto de cuadros sindrómicos que cursan con alteraciones de las glándulas ecrinas (displasia ectodérmica hidrótica, síndrome de SCHöPF-SCHULZ-PASSARGE) (55)(56)(57)(58)(59). Incluso se ha sugerido, en función de algunas observaciones, una eventual afectación de caracter más sistematizado, con implicación cutáneo-mucosa y patologías internas asociadas (60).…”