Dermatitis as a presenting sign of cystic fibrosis

Darmstadt, Gary L.

doi:10.1001/archderm.128.10.1358

Cited by 19 publications

(31 citation statements)

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“…Pulmonary and gastrointestinal components complicate the condition later. The skin lesions may resolve following administration of pancreatic enzymes and nutritional supplements 29,30 …”

Section: Clinical Featuresmentioning

confidence: 99%

Erythroderma/generalized exfoliative dermatitis in pediatric practice: An overview

Sehgal¹,

Srivastava²

2006

Int J Dermatology

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“…Pulmonary and gastrointestinal components complicate the condition later. The skin lesions may resolve following administration of pancreatic enzymes and nutritional supplements 29,30 …”

Section: Clinical Featuresmentioning

confidence: 99%

Erythroderma/generalized exfoliative dermatitis in pediatric practice: An overview

Sehgal¹,

Srivastava²

2006

Int J Dermatology

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“…The clinical picture of kwashiorkor is not uniform, and its differentiation from other nutritional dermatoses is not always clear‐cut. It has been suggested that in some patients, namely those with cystic fibrosis, the rash thought to be due to protein deficiency may actually be caused by a complex interaction between multiple nutritional deficits ( 27, 28). This has prompted research into a possible pathophysiological link that could account for similar skin findings arising from multiple insults.…”

Section: Discussionmentioning

confidence: 99%

“…A plethora of diseases exist in young children which may present with an eczematous, scaly, or desquamative dermatosis, including inborn errors of metabolism and immunodeficiency disorders ( Table 1) ( 16, 172138–41). Furthermore, when one is considering the diagnosis of kwashiorkor, there are a number of associated or underlying factors which the physician should be careful to keep in mind ( Table 2) ( 17, 22, 27, 28, 38). Of these, cystic fibrosis and other diseases of malabsorption have been the most often reported in the literature, but catabolic states as well as psychiatric disease and neurologic disorders, as seen in our patient, should always be considered.…”

Section: Discussionmentioning

confidence: 99%

Dermatosis in a Child with Kwashiorkor Secondary to Food Aversion

Eastlack

Grande

Levy

et al. 1999

Pediatric Dermatology

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Kwashiorkor is a common affliction of children worldwide. It occurs less often in developed countries, but has been reported under a variety of circumstances, including poverty, neurologic disease, and malabsorption. Because of its rare occurrence in the United States and because the affected child has an edematous rather than wasted appearance, physicians often do not consider it as a diagnostic entity. This article describes a case of kwashiorkor in a child with food aversion that manifested as "flaky paint dermatitis." Our discussion will attempt to delineate underlying conditions that may predispose to kwashiorkor. In addition, biochemical and cellular etiologic factors that may be linked with classical and nonclassical skin findings of kwashiorkor are considered. Finally, we present a differential diagnosis for any child with a generalized eczematous or desquamative rash. Our aim is to increase the ability of health care providers to identify and treat children with kwashiorkor in a timely manner.

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“…The involvement of these factors in the symptoms of the CFpatient with EFAD is only partially defined. It has been shown to be associated with dermatological symptoms (24), renal dysfunction (25) and liver steatosis (26). Treatment of EFAD has also been shown to improve the lung function in these patients (27).…”

Section: Essential Fatty Acid Deficiency (Efad)mentioning

confidence: 99%

Nutritional management in cystic fibrosis

Garemo

Strandvik

1999

Näringsforskning

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Cystic fibrosis (CF) is the most common hereditary fatal disease but the survival rate has improved markedly over the past 30 years. The three main reasons include specialised knowledge by centralisation of medical treatment, improved treatment of the bacterial infections in the lungs and the increased awareness of the importance of nutrition. Different factors, which affect the nutritional status have to be considered when nutritional recommendations in cystic fibrosis are given. These factors are abnormal metabolism, malabsorption and a decreased intake. An ordinary diet with a high mixed fat content including essential fatty acids together with supplement of fat soluble vitamins in water dispersion, are the basic in the nutritional treatment of the disease.

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Dermatitis as a presenting sign of cystic fibrosis

Cited by 19 publications

References 0 publications

Erythroderma/generalized exfoliative dermatitis in pediatric practice: An overview

Erythroderma/generalized exfoliative dermatitis in pediatric practice: An overview

Dermatosis in a Child with Kwashiorkor Secondary to Food Aversion

Nutritional management in cystic fibrosis

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