2010
DOI: 10.1055/s-0030-1250102
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Abstract: This report describes a rare case of left pulmonary agenesis associated with congenital diaphragmatic hernia and congenital heart disease in a 2-year-old child with pulmonary hypertension. We performed direct radical correction of the congenital heart defect. The postoperative course was challenging but without major complications.

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Cited by 6 publications
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“…Pulmonary agenesis is associated with numerous additional congenital abnormalities of the cardiovascular, musculoskeletal, genitourinary, and gastrointestinal systems that may negatively impact prognosis. Pediatric PA patients also present with varying degrees of Pulmonary Hypertension (PH) [2][3][4][5][6][7][8], but effects of PH on disease course and prognosis are uncertain, and there are no widely accepted treatment standards. Therefore, we describe five pediatric cases born with unilateral PA who developed PH, and review already published cases for a more complete description of disease features, clinical course, and treatment options.…”
Section: Introductionmentioning
confidence: 99%
“…Pulmonary agenesis is associated with numerous additional congenital abnormalities of the cardiovascular, musculoskeletal, genitourinary, and gastrointestinal systems that may negatively impact prognosis. Pediatric PA patients also present with varying degrees of Pulmonary Hypertension (PH) [2][3][4][5][6][7][8], but effects of PH on disease course and prognosis are uncertain, and there are no widely accepted treatment standards. Therefore, we describe five pediatric cases born with unilateral PA who developed PH, and review already published cases for a more complete description of disease features, clinical course, and treatment options.…”
Section: Introductionmentioning
confidence: 99%