Bullous Urticaria Pigmentosa

Robbins, Jack G.

doi:10.1001/archderm.1954.01540200092009

Cited by 17 publications

(1 citation statement)

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“…In another series, 16 of 43 patients (37%) had leukemia that was approximately equally divided among mast cell leukemia, myeloid leukemia, and monocyfic leukemia (22). We were unable to find any documented cases of mast cell leukemia or other form of leukemia developing in a patient with diffuse cutaneous mastocytosis (1,9,(23)(24)(25)(26)(27)(28)(29)(30)(31).…”

Section: Casementioning

confidence: 84%

Bullous Mastocytosis: Diffuse Cutaneous Mastocytosis with Extensive Blisters Mimicking Scalded Skin Syndrome or Erythema Multiforme

Golitz

Weston

Lane

1984

Pediatric Dermatology

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Bullous mastocytosis (diffuse cutaneous mastocytosis) is a rare form of mast cell disease that begins during the first month of life and causes extensive blisters that mimic scalded skin syndrome or bullous erythema multiforme. Discrete pigmented macules, papules, and nodules are absent and the characteristic leathery induration of skin may not develop until 6 months of age. Skin biopsy shows a subepidermal blister with mast cells at the base. The most serious complications are gastrointestinal hemorrhage and shock. The symptoms of bullous mastocytosis may be modified by a number of new therapeutic agents.

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Section: Casementioning

confidence: 84%

Bullous Mastocytosis: Diffuse Cutaneous Mastocytosis with Extensive Blisters Mimicking Scalded Skin Syndrome or Erythema Multiforme

Golitz

Weston

Lane

1984

Pediatric Dermatology

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Bullous Urticaria Pigmentosa in Infancy

Miller¹,

Shapiro²

1965

Arch Dermatol

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Atypical Diffuse Cutaneous Mastocytosis

Sahihi¹

1972

Arch Pediatr Adolesc Med

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A 19-month-old boy was found to have atypical diffuse cutaneous mastocytosis. Although severe dermographism and pressure urticaria were present from early infancy, his disease remained undiagnosed because he lacked the characteristic bullous and pigmented lesions of urticaria pigmentosa and the pebbly skin texture usually found in diffuse cutaneous mastocytosis. A skin biopsy from clinically normal skin disclosed a dense infiltrate of mast cells in the upper dermis.Since involvement of other organ systems is frequent in this form of mastocytosis, the patient was studied for internal lesions but none was found at this time. Parents of affected children should be informed that trauma to the skin such as brisk toweling after a bath, and drugs such as aspirin, codeine, and polymyxin B sulfate may precipitate episodes of histamine shock due to degranulation of the mast cells. Urticaria pigmentosa, originally described by Nettleship in 1869,' is characterized by an abnormal prolif¬ eration and infiltration of mast cells in the skin with occasional involve¬ ment of other organ systems. Al¬ though it is a relatively uncommon disease, the distinctive lesions of this disorder are usually recognized with¬ out difficulty in most infants and chil¬ dren. Occasionally, however, diag-

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Bullous Urticaria Pigmentosa

Cited by 17 publications

References 0 publications

Bullous Mastocytosis: Diffuse Cutaneous Mastocytosis with Extensive Blisters Mimicking Scalded Skin Syndrome or Erythema Multiforme

Bullous Mastocytosis: Diffuse Cutaneous Mastocytosis with Extensive Blisters Mimicking Scalded Skin Syndrome or Erythema Multiforme

Bullous Urticaria Pigmentosa in Infancy

Atypical Diffuse Cutaneous Mastocytosis

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