Associação de imunodeficiências primárias com doenças auto-imunes na infância

Abstract

Introduction: Rheumatologic findings may be the first manifestation of primary humoral immunodeficiencies. The frequency of selective IgA deficiency in patients with juvenile idiopathic arthritis (JIA like) and juvenile systemic lupus erithematosus (JSLE) is 2% to 4% and 1% to 4%, respectively. Objective: To describe patients with primary humoral immunodeficiencies associated with arthritis and to determine the prevalence of selective IgA deficiency within JIA and JSLE patients. Patients and methods: From