Assessment of children with vascular ring

Tola, Hasan Tahsin; Öztürk, Erkut; Yıldız, Okan; Erek, Ersin; Türkvatan, Aysel; Ergül, Yakup; Güzeltaş, Alper; Bakır, İhsan

doi:10.1111/ped.13101

Cited by 28 publications

(30 citation statements)

References 15 publications

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“…Moreover, scenario with the more serious symptoms allows to establish diagnosis in the younger age [1]. Diagnostic difficulties arise with patient age.…”

Section: Discussionmentioning

confidence: 99%

“…Chest X-ray and barium swallow X-ray are used for the first step of the diagnostic workups. However, chest computed tomography, magnetic resonance imaging give more data about anatomy of vascular rings and its relation to adjacent structures [1,13], whereas flexible bronchoscopy examination determines the degree of the tracheal compression and identifies tracheomalacia and/or bronchomalacia.…”

Section: Discussionmentioning

confidence: 99%

“…pulmonary sling). They cause compression of the trachea or/and the esophagus and therefore result in symptoms like inspiratory stridor, cough, wheezing, recurrent respiratory tract infections or dysphagia [1][2][3][4]. Diagnosis is usually established in the first year of life [2] -but in some cases, the correct diagnosis can be delayed for many years, especially when vascular rings produce less severe symptoms or symptoms mimicking other diseases (most of all asthma).…”

Section: Introductionmentioning

confidence: 99%

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Sarcoidosis-Associated Pulmonary Hypertension Treated with Sildenafil

Kusak

Cichocka‐Jarosz

Jedynak-Wąsowicz

et al. 2017

Advances in Respiratory Medicine

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Vascular rings are congenital defects of great vessels. They cause compression of the trachea or/and the esophagus and therefore result in symptoms like inspiratory stridor, cough, wheezing, recurrent respiratory tract infections or dysphagia. In some cases, the correct diagnosis can be delayed for many years, especially when vascular rings produce less severe symptoms or symptoms mimicking other diseases (most of all asthma). In this article, we would like to emphasis the usefulness of pulmonary function test (spirometry) in the initial diagnosis of vascular rings in school-aged children, as well as the importance of spirometry in evaluating patients with asthma presumption.

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“…Moreover, scenario with the more serious symptoms allows to establish diagnosis in the younger age [1]. Diagnostic difficulties arise with patient age.…”

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

See 1 more Smart Citation

Sarcoidosis-Associated Pulmonary Hypertension Treated with Sildenafil

Kusak

Cichocka‐Jarosz

Jedynak-Wąsowicz

et al. 2017

Advances in Respiratory Medicine

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“…Variants of these embryological regression result in an abnormal anatomy of the large arteries, that may form a complete or incomplete vascular ring encircling the trachea and esophagus. The vascular compression on the latter structures causes the typical respiratory symptoms or swallow dysfunction patients with a vascular ring present with …”

Section: Introductionmentioning

confidence: 99%

“…The true prevalence of vascular rings is unknown since not all rings have a clinical impact, but they are assumed to represent around 1% of cardiovascular congenital anomalies …”

Section: Introductionmentioning

confidence: 99%

The long‐term outcome of an isolated vascular ring – A single‐center experience

Depypere

Proesmans

Cools

et al. 2019

Pediatric Pulmonology

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Background and Objectives The aim of this study is to document the long‐term outcome of patients with a vascular ring. Methods A single‐center retrospective review of clinical symptoms was conducted in all patients born between 1980 and 2013, diagnosed with a complete vascular ring and at least 2 years of follow‐up. Data were extracted from patient files and clinical symptoms were assessed by questionnaires sent to the parents. Age and diagnostic tools, type of surgery, postoperative complications, and the prevalence of clinical symptoms (stridor at rest, stridor with exercise, cough, exercise intolerance, dysphagia, and frequent respiratory infections) were reviewed. Results Fifty‐one patients were included. The diagnosis was made before the age of 2 in 35/51. Surgery was performed in 41/51 patients with a limited number of reversible complications. The median follow‐up was 8 (IQR 5‐12) years. After 2 years, 21/51 patients were asymptomatic: 2/7 asymptomatic patients at diagnosis became symptomatic and symptoms resolved in 16/44 initially symptomatic patients. Consequently, 30/51 patients still had symptoms after 2 years. Of these, 16 had partial improvement, 5 stable symptoms, and 9 aggravation of symptoms. After 10 years, 26/36 patients were free of complaints. The most frequent long‐term symptom was stridor. Conclusion Surgical treatment of a congenital vascular ring is safe and mostly performed in patients with a double aortic arch. Conservative treatment for patients with little symptoms seems to be justifiable. A considerable number of patients have residual long‐term symptoms after surgical relief of the vascular ring.

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