Amiloidosis. También una enfermedad del corazón

García‐Pavía, Pablo; Tome-Esteban, M; Rapezzi, Claudio

doi:10.1016/j.recesp.2011.05.003

Cited by 69 publications

(60 citation statements)

References 82 publications

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“…Под старческим амилоидозом сердца понимают дикий ATTR (системный) или AANF типы. Поражение серд ца возможно также у 5% больных АА-амилоидо-зом [2].…”

Section: Methodsunclassified

“…Печень, селезенка не увеличены. В ана-лизах крови -небольшой лейкоцитоз (10-11 тыс) без сдвига формулы влево, СОЭ 16-34 мм/час, СРБ 1,42 мг/дл, креатинин 1,04 мг/дл, СКФ (CKD-EPI) 55 мл/мин/1,73 м 2 , РФ и АЦЦП в пределах нормы. При спирометрии выявлены обструктивные нарушения легкой степени, ЖЕЛ 78%.…”

Section: рис 3 результаты обследования больной а (Al-амилоидоз серunclassified

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Clinical Masks of Amyloidosis With the Heart Involvement: Modern Diagnostic Issues

Недоступ¹,

Седов²,

Kogan³

et al. 2017

Russ J Cardiol

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Section: Methodsunclassified

Section: рис 3 результаты обследования больной а (Al-амилоидоз серunclassified

Clinical Masks of Amyloidosis With the Heart Involvement: Modern Diagnostic Issues

Недоступ¹,

Седов²,

Kogan³

et al. 2017

Russ J Cardiol

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“…Existen cinco tipos de amiloidosis que comprometen al corazón: la amiloidosis primaria de cadena ligera (AL), la amiloidosis familiar, la amiloidosis sistémica senil, la amiloidosis atrial aislada y la amiloidosis sistémica secundaria (3,4) .…”

Section: Introductionunclassified

Amiloidosis cardiaca: reporte de un caso

et al. 2018

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Cardiac amyloidosis is a rare clinical entity and, therefore, almost unknown. It shows as a restrictive cardiomyopathy, since it is an infiltrative disease caused by the extracellular deposition of amyloids in the cardiac wall. Although it may be systemic, the heart condition determines its poor prognosis. This is the case of a 38-year-old patient who was admitted for dyspnea and severe fatigue. He was diagnosed with IgA multiple myeloma, lambda light chains, clinical stage IIIB, and initiated treatment with cyclophosphamide, thalidomide and dexamethasone. The patient stopped the treatment, and returned after one year and 2 months with an advanced disease and presence of amyloidosis. The patient progressed torpidly and eventually died. A review of the medical literature is performed concerning amyloidosis types, physiopathology, diagnostic methods and treatment.

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“…Treatment of cardiac amyloidosis is based on the relief of symptoms and, when feasible, in the reduction of the amyloid production with the aid of chemotherapy or bone marrow transplantation 4 , 6…”

Section: Introductionmentioning

confidence: 99%

Cardiac amyloidosis: a challenging diagnosis

Morais¹,

Arruda²,

Bonadia³

et al. 2014

ACR

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Cardiovascular involvement of amyloidosis is present in 90% of cases, which is frequently associated with the primary form of the disease (AL amyloidosis). Clinical manifestations are represented by heart failure due to restrictive myocardiopathy and electrical impulse conduction abnormalities, which are clinically remarkable in up to 50% of the cases. The prognosis of patients with systemic amyloidosis is directly associated with the presence of cardiac involvement, such that survival does not usually exceed 4 months after the onset of heart failure signs and symptoms. The authors report a case of primary systemic amyloidosis, diagnosed only at autopsy, with severe cardiac involvement.

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Amiloidosis. También una enfermedad del corazón

Cited by 69 publications

References 82 publications

Clinical Masks of Amyloidosis With the Heart Involvement: Modern Diagnostic Issues

Clinical Masks of Amyloidosis With the Heart Involvement: Modern Diagnostic Issues

Amiloidosis cardiaca: reporte de un caso

Cardiac amyloidosis: a challenging diagnosis

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