Abnormal Brain-Stem Auditory Evoked Potentials Following Ondine's Curse

Congenital central hypoventilation syndrome: An update

“…Based on the initial premise that a centrally located defect is present in CCHS, it is not surprising that over the years multiple attempts, albeit unsuccessful, have been made to identify structural central nervous system abnormalities. Earlier reports of hypoplasia of the arcuate nucleus in one patient with CCHS, 39 and the presence of abnormal evoked potential responses to auditory stimuli [40][41][42] have further suggested that a brainstem lesion may be present. In addition, central hypoventilation syndrome has been reported in occasional patients with cerebrovascular malformations, [43][44][45][46][47] and in patients with central nervous system infections.…”

Congenital central hypoventilation syndrome: An update

“…Based on the initial premise that a centrally located defect is present in CCHS, it is not surprising that over the years multiple attempts, albeit unsuccessful, have been made to identify structural central nervous system abnormalities. Earlier reports of hypoplasia of the arcuate nucleus in one patient with CCHS, 39 and the presence of abnormal evoked potential responses to auditory stimuli [40][41][42] have further suggested that a brainstem lesion may be present. In addition, central hypoventilation syndrome has been reported in occasional patients with cerebrovascular malformations, [43][44][45][46][47] and in patients with central nervous system infections.…”

Dopamine D2-Like Receptors Modulate Unconditioned Fear: Role of the Inferior Colliculus

“…These potentials reflect neuronal activity in the auditory complex, mainly in the cochlear nucleus, superior olive, and IC [26]. Previous studies have shown that AEPs generated in the IC are sensitive to aversive manipulations [7], [27], [28].…”

Congenital central hypoventilation syndrome in children: a Hong Kong perspective

“…Central hypoventilation syndrome may be congenital or the result of trauma/injury and neurodegeneration. 13 For example, abnormal brainstem auditory evoked responses were observed in a woman with alcoholism who recovered from CCHS. 13 Most congenital cases are identified in neonates.…”

“…13 For example, abnormal brainstem auditory evoked responses were observed in a woman with alcoholism who recovered from CCHS. 13 Most congenital cases are identified in neonates.…”

Congenital central hypoventilation syndrome: An update

“…Based on the initial premise that a centrally located defect is present in CCHS, it is not surprising that over the years multiple attempts, albeit unsuccessful, have been made to identify structural central nervous system abnormalities. Earlier reports of hypoplasia of the arcuate nucleus in one patient with CCHS, 39 and the presence of abnormal evoked potential responses to auditory stimuli [40][41][42] have further suggested that a brainstem lesion may be present. In addition, central hypoventilation syndrome has been reported in occasional patients with cerebrovascular malformations, [43][44][45][46][47] and in patients with central nervous system infections.…”

Dopamine D2-Like Receptors Modulate Unconditioned Fear: Role of the Inferior Colliculus

“…These potentials reflect neuronal activity in the auditory complex, mainly in the cochlear nucleus, superior olive, and IC [26]. Previous studies have shown that AEPs generated in the IC are sensitive to aversive manipulations [7], [27], [28].…”

Congenital central hypoventilation syndrome in children: a Hong Kong perspective

“…Central hypoventilation syndrome may be congenital or the result of trauma/injury and neurodegeneration. 13 For example, abnormal brainstem auditory evoked responses were observed in a woman with alcoholism who recovered from CCHS. 13 Most congenital cases are identified in neonates.…”

“…13 For example, abnormal brainstem auditory evoked responses were observed in a woman with alcoholism who recovered from CCHS. 13 Most congenital cases are identified in neonates.…”

Congenital central hypoventilation syndrome: An update

“…Based on the initial premise that a centrally located defect is present in CCHS, it is not surprising that over the years multiple attempts, albeit unsuccessful, have been made to identify structural central nervous system abnormalities. Earlier reports of hypoplasia of the arcuate nucleus in one patient with CCHS, 39 and the presence of abnormal evoked potential responses to auditory stimuli [40][41][42] have further suggested that a brainstem lesion may be present. In addition, central hypoventilation syndrome has been reported in occasional patients with cerebrovascular malformations, [43][44][45][46][47] and in patients with central nervous system infections.…”

Dopamine D2-Like Receptors Modulate Unconditioned Fear: Role of the Inferior Colliculus

“…These potentials reflect neuronal activity in the auditory complex, mainly in the cochlear nucleus, superior olive, and IC [26]. Previous studies have shown that AEPs generated in the IC are sensitive to aversive manipulations [7], [27], [28].…”

Congenital central hypoventilation syndrome in children: a Hong Kong perspective

“…Central hypoventilation syndrome may be congenital or the result of trauma/injury and neurodegeneration. 13 For example, abnormal brainstem auditory evoked responses were observed in a woman with alcoholism who recovered from CCHS. 13 Most congenital cases are identified in neonates.…”

“…13 For example, abnormal brainstem auditory evoked responses were observed in a woman with alcoholism who recovered from CCHS. 13 Most congenital cases are identified in neonates.…”