The management of knee dislocation in a child with Larsen syndrome

Kaissi, Ali Al; Rudolf, G.; Klaushofer, Klaus; Grill, Franz

doi:10.1590/s1807-59322011000700030

Cited by 16 publications

(8 citation statements)

References 19 publications

(22 reference statements)

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“…But multiple congenital joint dislocations and facial abnormalities characteristic of Larsen syndrome are absent in smallpox. Absence of joint deformities before the onset of fever with rash and the lack of typical facial profile rules out Larsen syndrome [ 13 ]. Moreover, in smallpox the possible growth disorders have a varied layout.…”

Section: Discussionmentioning

confidence: 99%

Excellent Functionality Despite Clinico-Radiological Deformity in Osteomyelitis Variolosa - A Case Report

Mugalur

Shahane

Samant

et al. 2015

TOORTHJ

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Despite the eradication of smallpox from the world in 1980 the osteo-articular sequelae of smallpox are still occasionally noticed in previously endemic areas. The sequelae of osteomyelitis variolosa may raise a diagnostic challenge to the untrained eyes of the surgeon. We present a case of “osteomyelitis variolosa” in a 70 years old patient. The patient had bilateral dislocation of the elbow joint with multidirectional instability. There was distortion of the articular surfaces and ankylosis of the bilateral proximal radio-ulnar joint. Hypoplasia of the right ulna with short fourth and fifth metacarpals of the left hand and hypoplasia of right fourth metacarpal with cortical thickening was noted radiologically. The patient had minimal disability of his elbows despite the striking radiological abnormality and was functionally independent.

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Section: Discussionmentioning

confidence: 99%

Excellent Functionality Despite Clinico-Radiological Deformity in Osteomyelitis Variolosa - A Case Report

Mugalur

Shahane

Samant

et al. 2015

TOORTHJ

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“…Se e quando o gesso falhar, o tratamento cirúrgico consiste em quadriceplastia, mini tenotomia do quadríceps aberta, banda iliotibial (IT) e liberação capsular e avanço do ligamento cruzado anterior (LCA). 5 No entanto, é importante que em anomalias musculoesqueléticas associadas concomitantes, o joelho seja sempre manipulado e tratado primeiro, antes do pé ou do quadril.…”

Section: Introductionunclassified

Luxação congênita do joelho no nascimento - Um caso extraordinário de redução espontânea

KUMAR

Arumugam

Azuatul

et al. 2020

Rev Bras Ortop (Sao Paulo)

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ResumoA luxação congênita do joelho (LCJ) é uma malformação rara caracterizada por deformidade de hiperextensão do joelho com deslocamento anterior da tíbia, presente ao nascimento. Raramente relatada, a LCJ pode ocorrer como uma deformidade isolada ou comumente associada a anormalidades musculoesqueléticas, sendo as mais comuns a displasia do desenvolvimento do quadril (DDQ) e o pé torto congênito (PTC). A etiologia é desconhecida, mas a LCJ foi associada a certos fatores intrínsecos e extrínsecos. O tratamento com métodos conservadores em um estágio inicial tem maior probabilidade de produzir resultados bem-sucedidos. Relatamos aqui um caso raro de redução espontânea bem-sucedida de LCJ em um bebê nas suas primeiras 24 horas de vida.

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“…Characteristic findings of the disorder include short stature, dislocations of the large joints [1, 6] (hips, knees, elbows, frequently bilateral) and various other skeletal malformations of the hands (spatulate), feet (equinovarus, hind foot valgus) and spine (instability, hypodontia, kyphosis, scoliosis) [7-10]. Distinctive facial features include frontal bossing, midface hypoplasia with depression of the nasal bridge, and ocular hypertelorism [1, 11].…”

Section: Introductionmentioning

confidence: 99%

One Stage Bilateral Total Hip Arthroplasty in Siblings with Larsen Syndrome

Merle¹,

Waldstein²,

Lipman³

et al. 2016

Open Orthopaedics J.

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Background:Larsen syndrome is a rare genetic disorder caused by congenital weakness of the connective tissues. It can present with a variety of musculoskeletal and cardiovascular abnormalities. The current report describes two siblings with Larsen Syndrome who presented with severe bilateral hip arthritis and underwent one stage bilateral total hip arthroplasty (THA). The aim was to report on the clinical features of Larsen Syndrome and their implications for total hip replacement surgery.Methods:Two siblings, a 32 year-old female and a 30 year-old male, presented with severe bilateral hip arthritis and a history of Larsen Syndrome. Both patients underwent a detailed, multidisciplinary preoperative medical work up and radiological imaging including computer tomography. All four hips were operated using a cementless primary press-fit cup (Pinnacle, DePuy, Warsaw, IN) and a cementless modular stem system (S-ROM, DePuy, Warsaw, IN) utilizing a posterior approach. Prophylactic cerclages wires were placed proximal to the lesser trochanter before stem preparation and bone grafting of bone cysts in the greater trochanter was performed in all four hips.Results:After 2 years both patients reported significant improvements of function, pain and quality of life. The Oxford hip score improved from preoperative 21 (range 12-24) points up to 39 (range 38-41) points at 2-year follow up. Radiographic follow-up showed good graft incorporation and no signs of implant loosening.Conclusion:The current case report suggests that one stage bilateral THA is a feasible treatment option for young adults with Larsen syndrome and secondary arthritis of the hip.

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The management of knee dislocation in a child with Larsen syndrome

Cited by 16 publications

References 19 publications

Excellent Functionality Despite Clinico-Radiological Deformity in Osteomyelitis Variolosa - A Case Report

Excellent Functionality Despite Clinico-Radiological Deformity in Osteomyelitis Variolosa - A Case Report

Luxação congênita do joelho no nascimento - Um caso extraordinário de redução espontânea

One Stage Bilateral Total Hip Arthroplasty in Siblings with Larsen Syndrome

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