2007
DOI: 10.1590/s1806-37132007000300017
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Abstract: Pulmonary amyloidosis is a rare disease, characterized by extracellular deposition of fibrillary protein in the lungs. Amyloidosis is a generic term for a heterogeneous group of diseases, including Alzheimer's disease and type 2 diabetes mellitus. In the respiratory system, it appears in various forms: tracheobronchial; nodular pulmonary; and alveolar septal (diffuse parenchymal). We present the case of a woman who was a 20 pack-year smoker and had nodular pulmonary amyloidosis, as diagnosed through tests perf… Show more

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Cited by 4 publications
(5 citation statements)
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References 9 publications
(20 reference statements)
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“…In certain diseases, the clinically significant amyloid deposition can be limited to one organ. [20][21][22] The involvement of kidneys repeatedly presents only as asymptomatic proteinuria or nephrotic syndrome. However, the primary deposition may be confined to blood vessels or tubules with progression to renal failure with little or no proteinuria.…”
Section: Resultsmentioning
confidence: 99%
See 1 more Smart Citation
“…In certain diseases, the clinically significant amyloid deposition can be limited to one organ. [20][21][22] The involvement of kidneys repeatedly presents only as asymptomatic proteinuria or nephrotic syndrome. However, the primary deposition may be confined to blood vessels or tubules with progression to renal failure with little or no proteinuria.…”
Section: Resultsmentioning
confidence: 99%
“…Amyloidosis is a generic term for a heterogeneous group of associated diseases with abnormal deposition of fibrillar proteins. 20 It is classified according to the type of precursor protein that form amyloid fibrils and distribution of amyloid deposition in a localized form or systemically. 20 The clinical manifestations of amyloidosis depend on the type of precursor protein, its tissue distribution, and amount of deposition of the amyloid substance.…”
Section: Discussionmentioning
confidence: 99%
“…3 As primeiras são localizadas e a última sistémica. 4,6 Em casos raros pode também atingir a pleura, gânglios intratorácicos e os vasos. 1 A localização mais comum é a laríngea e a traqueobrôn-quica, sob a forma de nódulos pseudo-tumorais (15%) ou de placas submucosas multifocais (85%).…”
Section: Discussionunclassified
“…A imunohistoquímica identifica o tipo de fibrilas, mas não foi realizada nos casos descritos. 1,4 O diagnóstico de amiloidose sistémica implica a realização de biopsia, sendo que o estudo da gordura peri-umbilical ou do recto apresentam uma sensibilidade superior a 90%.…”
unclassified
“…Dessa feita, destaca-se a raridade do acometimento pulmonar pela Amiloidose, a qual se classifica em quatro variantes, à depender do local e grau de acometimento, são elas: Amiloidose traqueobrônquica localizada ou difusa e Amiloidose parenquimatosa nodular ou difusa 2 . Essa doença transita desde um mero achado acidental, até um acometimento grave que pode cursar com óbito 3 .…”
Section: Introductionunclassified