2009
DOI: 10.1590/s1516-84842009005000012
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Abstract: IntroduçãoA doença falciforme caracteriza-se por uma alteração geneticamente determinada na produção da hemoglobina, formando a hemoglobina S (HbS)A. 1 HbS sofre polimerização em situações de estresse oxidativo, alterando a capacidade de deformabilidade e a plasticidade da hemácia, que assume o formato de foice. 2 Com isto, há maior risco de provocarem fenômenos vasooclusivos, principais responsáveis pela sintomatologia apresentada pelos homozigotos. 1 As manifestações clínicas envolvem crises dolorosas, síndr… Show more

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Cited by 8 publications
(9 citation statements)
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“…(12,29) Being a frequent complication, family members should be taught to recognize the origin and intensity of pain in order to take appropriate measures. (25) Another important cause of hospitalization in this study was acute splenic sequestration.…”
Section: Discussionmentioning
confidence: 99%
“…(12,29) Being a frequent complication, family members should be taught to recognize the origin and intensity of pain in order to take appropriate measures. (25) Another important cause of hospitalization in this study was acute splenic sequestration.…”
Section: Discussionmentioning
confidence: 99%
“…Research conducted in the Gaza Strip, in the Palestinian Territories, showed that 61% of the collections occurred between the 11th and 17th day of life 18 . In Brazil, in Porto Alegre city, the average was 11 days; 19 in Sergipe State 17 days, with 50% of samples being collected in children older than 28 days; 20 in Campina Grande city, the average was 29.8 days, 21 and in Marília, São Paulo State, the average was 27 days 22 …”
Section: Discussionmentioning
confidence: 99%
“…As manifestações clínicas podem variar, sendo assintomáticas nos primeiros seis meses de vida do portador da doença devido à presença de hemoglobina fetal (Hbf), como também sintomáticas, evidenciados por quadros de crises dolorosas, síndrome torácica aguda, AVC, úlceras de pernas e anemia hemolítica (MENDONÇA et al, 2008).…”
Section: Anemia Falciforme E Outras Hemoglobinopatiasunclassified
“…Também é indicado que se faça a vacina antipneumocócica conjugada 7 com esquema de 2, 4 e 6 meses de idade e reforço entre 12 e 15 meses de idade. Além das vacinas contra o Haemophilus influenzae tipo b e contra meningite tipo C conjugada (MENDONÇA, et al, 2008). …”
Section: Anemia Falciforme E Outras Hemoglobinopatiasunclassified