2002
DOI: 10.1590/s0041-87812002000200004
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Abstract: The authors report a case of primary rhabdomyosarcoma of the diaphragm, an extremely rare presentation with only 14 cases reported in the literature. An 18-year-old male presented 2 spontaneous occurrences of pneumothorax. Computed tomography and magnetic resonance showed a tumoral mass on the right diaphragmatic surface, and after biopsy, the diagnosis was compatible with spindle cell rhabdomyosarcoma. Because the visceral pleura was invaded by the tumoral mass, a right pleuropneumonectomy was performed. The … Show more

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Cited by 13 publications
(8 citation statements)
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References 21 publications
(25 reference statements)
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“…Indications for full thickness resection and diaphragmatic repair include primary tumors such as leio-or rhabdomyosarcoma, primary or secondary malignancies of the chest with direct invasion as well as extensive extrathoracic neoplastic disease, traumatic rupture and congenital aplasia [1][2][3][4][5][6]. A wide range of synthetic, biological, autologous and even bioartificial materials are available, and are mostly chosen on the basis of the surgeonʼs experience and preferences [2,3,7,8].…”
mentioning
confidence: 99%
“…Indications for full thickness resection and diaphragmatic repair include primary tumors such as leio-or rhabdomyosarcoma, primary or secondary malignancies of the chest with direct invasion as well as extensive extrathoracic neoplastic disease, traumatic rupture and congenital aplasia [1][2][3][4][5][6]. A wide range of synthetic, biological, autologous and even bioartificial materials are available, and are mostly chosen on the basis of the surgeonʼs experience and preferences [2,3,7,8].…”
mentioning
confidence: 99%
“…10 The alveolar subtype shows marked molecular genetic changes, unlike the embryonal one. 11 Here, the alveolar subtype shows recurrent chromosomal translocation, including t(2;13)(q35;q14) and less commonly t(1;13)(p36;q14). The t(2;13) translocation results in the fusion of part of the PAX3 gene to part of the FKHR gene, leading to the formation of the PAX3-FKHR gene that encodes a chimeri protein.…”
Section: Discussionmentioning
confidence: 96%
“…In children, the embryonal subtype is the most common (50-60 per cent), 4,10 in contrast to adults; and alveolar subtype is the most common subtype seen under age 25. 11 almost exclusively in adults. 4,6 The embryonal subtype is characterized by an admixture of undifferentiated, small, round or spindle-shaped cells with variable numbers of strap-shaped or tadpole-shaped eosinophilic rhabdomyoblasts.…”
Section: Discussionmentioning
confidence: 99%
“…Komplet rezeksiyon oranı düşüktür (22). Geniş görüş sağlaması nedeniyle öncelikle torakotomi kesisi kullanılırken, subkostal kesi, laparotomi (19) ve son dönemde ise hem tanı koymadaki üstünlüğü ile tedaviyi yönlendirmesi hem de minimal invaziv olması sebebi ile VATS +/-laparoskopi kullanılmaktadır (15).…”
Section: Tedavi̇unclassified