Arachnoid cysts of the posterior fossa represent a rare group of central nervous system lesions. Quadrigeminal cistern cysts, specifically, are unusual lesions, with only 79 cases described in the English literature [1][2][3][4][5][6][7][8] . Classical treatment of such lesions consists of craniectomy and fenestration of the lesion or cystoperitoneal shunting. Neuroendoscopy represents a new effective minimally invasive approach for such lesions.We report the case of a two year old boy who presented a quadrigeminal cyst arachnoid cyst which was successfully treated by neuroendoscopy in our department.
CASEA two-year-old boy, presented to our department with one month history of daily headaches, vomiting and gait instability. There was no report of recent associated infections, previous history of any classical childhood viral infection or alterations of psychomotor development. The exam at admission revealed a hypoactive child, obvious macrocrania and gait instability associated with lower limbs hypertonia. There was no papilloedema. There were no cranial nerves or sensitive alterations. Analysis of the cephalic perimeter growth curve showed mild upward deviation since the initial months of life. Computed tomography (CT) scan demonstrated supratentorial hydrocephalus associated with a cystic lesion in the posterior fossa. Magnetic resonance image (MRI) demonstarted enlargement of the supratentorial ventricular system secondary to a large quadrigeminal cistern arachnoid cyst compressing the brainstem, cerebellum, aqueduct of Sylvius and fourth ventricle (Fig 1). A ventriculo-peritoneal shunt was inserted at this time, with regression of the symptoms.Seven months later, the patient returned to our department with history of new episodes of headache and vomiting. A new MRI revealed persistence of the arachnoid cyst. It was decided to perform endoscopic fenestration of the cyst and third ventriculostomy for treatment of the hydrocephalus.Informed consent was obtained from the family and the patient underwent the surgical procedure. A paramedian incision was performed overlying the right coronal suture, 2.5 cm off the midline. Then a 14-mm burr hole was created and the dura-mater opened. After navigating through the right lateral ventricle and third ventricle, the arachnoid cyst was reached and cysto-ventricle shunting was realized. This was followed by a third ventriculostomy. There were no complications during the surgery. The patient presented no symptoms at time of discharge (Fig 2A).At one year follow-up, the patient was asymptomatic. Neurological examination was unremarkable (Fig 2B).
DISCUSSIONParacollicular arachnoid cyst, cysts posterior to the third ventricle, tentorial notch arachnoid cyst, cyst of cisterna ambiens, paramesencephalic cysts and parapineal