Background: The solid pseudopapillary neoplasm is a rare tumor of the pancreas. However, it´s
etiology still maintain discussions. Aim: To analyze it´s clinical data, diagnosis and treatment. Methods: A retrospective study of medical records of all patients treated from January
1997 until July 2015. Results: Were identified 17 cases. Most patients were women (94.11%) and the average age
was 32.88 years. The main complaint was abdominal mass (47.05%). The most frequent
location was in the body/tail of the pancreas (72.22%) and the most frequently
performed surgery was distal pancreatectomy with splenectomy (64.70%). No patient
had metastases at diagnosis. Conservative surgery for pancreatic parenchyma was
performed in only three cases. The rate of complications in the postoperative
period was 35.29% and the main complication was pancreatic fistula (29.41%). No
patient underwent adjuvant treatment. Conclusions: The treatment is surgical and the most common clinical presentation is abdominal
mass. Distal pancreatectomy with splenectomy was the most frequently performed
surgery for its treatment.