Tessier cleft 7, also known as Transverse facial cleft or congenital macrostomia, is a rare congenital anomaly. It presents with varying degree of severity and is associated with anomalies of other structures developing from first and second branchial arches. We report twelve cases of Tessier cleft 7 presenting to us at various ages. The cases were studied on the basis of antenatal and family history, age, sex, laterality, severity and other associated anomalies. The clefts were classified complete or incomplete on the basis of their lateral extension. Surgical correction of the clefts consisted of soft tissue repair and correction of associated deformities with satisfactory functional and aesthetic results, without any intra-operative and post-operative complications.
Cleft Lip and Palate and Rare Facial clefts occur in varying degree of severity and variety of patterns. It's a nightmare which every parent wants to avoid. Facial clefts occur when the structures contributing to the formation of face namely-the frontonasal prominence, the maxillary prominence, the medial nasal prominence, the lateral nasal prominence, and the mandibular prominences fail to fuse with one another. These defects result in abnormal facial appearance, difficulties in feeding, defective dentition, defective speech, repeated ear and respiratory tract infections, and social stigma. In this study, an attempt has been made to know the prevalence rate of Cleft Lip and Palate and Rare Facial clefts as well as its sexual dimorphism in upper (eastern) Assam. The study was carried out from January 2008 to June 2014 among the 781 cases of facial clefts who attended the Smile Train Centre in Srishti Hospitals, Dibrugarh, Upper Assam, India. It was found that isolated cleft lip (41.22%) occurred more commonly than isolated cleft palate (17.41%). Cleft lip was more common in males (63.97%) than in females (36.02%). 312 (39.94%) of the cases presented with both cleft lip and palate and among these 188 (60.25%) were females and 124 (39.74%) were males. Isolated cleft palate was found to be more common in females (68.38%) than in males (31.61%). All these cases underwent reconstructive surgery and left the hospital smiling with a sociably presentable face.
BACKGROUND Congenital anomalies of the digits include malformations like Polydactyly, Syndactyly, Brachydactyly, Macrodactyly, Cleft hand and foot (Lobster claw deformity), Constriction ring, Polysyndactyly, Thumb aplasia (Ectrodactyly) or Hypoplasia, etc. Among these, polydactyly is the commonest congenital deformity, presenting with a range of defects from minor soft tissue duplication to major bony abnormalities. Aim-The present study was aimed at studying the incidence of various types of anomalies of the digits in Dibrugarh district of Assam, India. MATERIALS AND METHODS This is a descriptive study. The study was carried out in patients attending the Plastic Surgery OPD at Assam Medical College & Hospital and at Srishti Hospitals & Research Centre, Dibrugarh, Assam from July 2014 to July 2017. We did an analysis of a total of 3850 patients for the presence of any congenital anomaly of digits. Of these, 2116 (54.96%) were male and 1734 (45.04%) were female. Those cases with congenital malformations of the digits were further investigated in detail for family history, maternal drug history during pregnancy, history of exposure to radiation during pregnancy, consanguinity, and associated congenital anomalies. The cases were photographed for record. RESULTS Among the 3850 patients included in the study, only 35 (0.91%) presented with noticeable anomalies of the fingers & toes. Of these, the commonest was polydactyly in 20 (57.14%) cases followed by syndactyly in 8 (22.56%) cases. We found macrodactyly (Foot) in 2 (5.71%) cases. 1 (2.86%) case each of polysyndactyly, brachydactyly, thumb aplasia, amniotic band amputation and lobster claw hand was found. CONCLUSION Congenital anomalies have always been a source of social stigma. Most of these anomalies can be corrected surgically.
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