Two patients with incomplete pentalogy of Cantrell are described. The first was a girl with a large omphalocele with evisceration of the heart, liver and intestines with an intact sternum. Echocardiography showed profound intracardiac defects. The girl died 33 h after birth. The second patient was a female fetus with ectopia cordis (EC) without intracardiac anomalies; a large omphalocele with evisceration of the heart, stomach, spleen and liver; a hypoplastic sternum and rib cage; and a scoliosis. The pregnancy was terminated.

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The management of premature, very low birth weight infants with esophageal atresia and tracheo-esophageal fistula complicated by respiratory insufficiency is still challenging. We present a case of a premature, very low weight infant in whom we used a technique of temporary gastric banding to control the air leak through the fistula.