-The clinical features of the primary progressive freezing gait, a rare and distinct neurological entity, have been described in some articles. This paper describes this gait disorder affecting one patient, whose condition's long course provoked no postural instability. As stated in the literature, the pathophysiology of the primary progressive freezing gait still remains unclear, although the lack of response to levodopa therapy suggests a possible involvement of nondopaminergic pathways. Alteration in the visual perception may be a potential cause for the condition.KEY WORDS: movement disorders, isolated freezing gait (primary, progressive).An isolated stubborn alteration of gait, with no signs of bradykinesia, rigidity, or tremor has been described in the literature as a "primary progressive freezing gait" (PPFG). This condition has been characterized as a hesitation to start walking, usually accompanied by festination, postural instability and recurrent falls that appear only while walking 1 . The condition also seems to be related to a distortion of unknown pathophysiology in relation to the visual perception of space 9 . A similar alteration was described by Atchison et al. 2 as "syndrome of gait ignition failure". However, this syndrome, differently from PPFG, presents normal equilibrium or slight alteration and no festination 2 . This is a case study of a male patient, 73 years old, with a long-term history of gait alteration, without postural instability or any other signs of parkinsonism. CASE REPORTA 73 year old man was evaluated during four years at the Movement Disorders Ambulatory, Department of Neurology, Hospital Universitário Pedro Ernesto, Universidade do Estado do Rio de Janeiro, Brazil. Nine years before, he noticed a slowly progressive change in his walk, characterized by some difficulty to lift the feet *Assistant Professor of Neurology, Universidade Gama Filho, Rio de Janeiro, Brasil; ** Joint Professor of Neurology, Faculdade de Ciências Médicas da Universidade do Estado do Rio de Janeiro (UERJ), Rio de Janeiro, Brasil; ***Neurologist, Rio de Janeiro, Brasil. Aceite: 5-abril-1997.Dr João Santos Pereira -Disciplina de Neurologia, Hospital Universitário Pedro Ernesto UERJ -Boulevard 28 de Setembro 77, 2 o andar -20551-030 Rio de Janeiro RJ -Brasil. Marcha congelada progressiva primária: relato de casoRESUMO -Uma rara e distinta entidade neurológica, a marcha congelada progressiva primária, tem sido relatada na literatura. Descrevemos o caso de um paciente com este distúrbio da marcha que, apesar do longo curso da doença, não apresentava instabilidade postural. Como citado na literatura, a fisiopatologia desta condição permanece obscura, embora a falta de resposta à levodopa sugira uma possível participação de vias não dopaminérgicas. Alteração na percepção visual também pode estar envolvida na gênese desta afecção.PALAVRAS CHAVE: desordens do movimento, marcha congelada isolada (primária, progressiva).
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